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題 名 | IgA Pemphigus: Subcorneal Pustular Dermatosis Type--A Case Report with Vesicle and Pustular Eruption for 13 Years Cured with Dapsone in 3 Weeks=角質層下膿疱性皮膚病亞型免疫球蛋白A天疱瘡--一例13年皮疹以Dapsone 3週治癒之病例報告 |
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作 者 | 劉勇佺; 宗天一; 林祺彬; 羅珮瑜; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 26:4 2008.12[民97.12] |
頁 次 | 頁258-263 |
分類號 | 415.765 |
關鍵詞 | 免疫球蛋白A天疱瘡; 自體免疫; 水疱; IgA pemphigus; Subcorneal pustular dermatosis; Monoclonal IgA gammopathy; |
語 文 | 英文(English) |
中文摘要 | 免疫球蛋白A(IgA)天瘡是一種新歸類的自體免疫皮膚水性疾病。其臨床表現為搔癢的水性與膿性皮疹,好發位置為身體對摩的部位(如腋下與腹股溝)。此類病人取皮膚病灶作直接免疫螢光染色可發現IgA在表皮細胞間沈積。然而,與尋常性天瘡相異的是,IgA天瘡的病程是比較輕微而且預後較好。我們提出一位角質層下膿性皮膚病亞型IgA天瘡合併單株IgA免疫球蛋白症的案例。此病人接受每日口服dapsone 50 mg治療三星期後,皮疹獲得顯著的改善,停藥後半年亦無復發現象。 |
英文摘要 | IgA pemphigus is a newly characterized group of autoimmune intraepidermal blistering diseases presenting as vesiculopustular eruptions with a predilection in axillary and groin areas. Immunopathologically, IgA deposition in the intercellular space of the epidermis is present in all cases of IgA pemphigus by direct immunofluorescence. However, unlike pemphigus vulgaris, IgA pemphigus carries a relatively benign course. Herein we reported a case of subcorneal pustular dermatosis type IgA pemphigus associated with monoclonal IgA gammopathy. The eruptions cleared with dapsone 50 mg daily for three weeks and no recurrence was found after 6-months follow-up. |
本系統中英文摘要資訊取自各篇刊載內容。