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題 名 | Pemphigus Foliaceus Resembling Seborrheic Keratosis=類似脂漏性角化症的落葉性天疱瘡 |
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作 者 | 黃沛盈; 朱家瑜; 王莉芳; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 25:3 2007.09[民96.09] |
頁 次 | 頁205-209 |
分類號 | 415.765 |
關鍵詞 | 落葉性天疱瘡; 自體免疫; 水疱; Pemphigus foliaceus; Postpemphigus acanthoma; Seborrheic keratosis; |
語 文 | 英文(English) |
中文摘要 | 落葉性天庖瘡是-慢性自體免疫水庖病,有不同的臨床表現。常見的表現包括紅斑與落屑、表淺糜爛、或有痂皮及鬆軟的水庖。然而落葉性天庖瘡少以類似脂漏性角化症的棕色疣狀突起表現。我們報告一個病人在軀幹有多個類似脂漏性角化症病灶,病理顯示角化過度、棘層肥厚、有乳突瘤狀增生以及上層表皮有棘層鬆解,與國外文獻報告雷同,然而首次報告於台灣落葉性天庖瘡病人。病灶的直接免疫螢光檢查顯示在表皮細胞間隙有IgG及C3沉澱。給予口服prednisolone、azathioprine、dapsone及局部類固醇後,病灶緩慢變平。 |
英文摘要 | Pemphigus foliaceus is a chronic autoimmune bullous disease with variable clinical presentations. Common manifestations of individual lesions are erythema with desquamation, superficial erosions with or without crusts or flaccid bullae. Hyperpigmented and verrucous lesions clinically resembling seborrheic keratosis lesions are rarely seen in patients with pemphigns foliaceus. We present a patient with multiple seborrheic keratosis-like lesions on the trunk with characteristic pathologic findings, which is first reported in Taiwan. The histology showed hyperkeratosis, acanthosis, and papillomatosis accompanied with acantholysis in the superficial epidermis. The direct immunofluorescence revealed IgG and C3 deposition in the intercellular spaces of epidermis. The lesions responded slowly to oral prednisolone, azathioprine, dapsone and topical clobetasol propionate treatment. |
本系統中英文摘要資訊取自各篇刊載內容。