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題 名 | 廣泛性毛囊缺陷瘤伴發於全身性紅斑性狼瘡=Generalized Hair Follicle Hamartoma Associated with Systemic Lupus Erythematosus |
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作 者 | 郭宏文; 林政宏; 何宜承; 黃純真; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 17:2 1999.06[民88.06] |
頁 次 | 頁184-190 |
分類號 | 415.761 |
關鍵詞 | 毛囊缺陷瘤; 全身性紅斑性狼瘡; Generalized hair follicle hamartoma; Alopecia; Systemic lupus erythematosus; Autoimmune disease; |
語 文 | 中文(Chinese) |
中文摘要 | 一位已有七年全身性紅斑性狼瘡病史的60歲台籍婦女,主訴在其臉上及耳朵出現 一些浸潤性丘疹及斑塊病灶,已有六個月之久。同時,過去六年來其頭髮、眉毛、腋毛及陰 毛有逐漸脫落的情形。從她右側鼻唇溝和耳朵的浸潤性斑塊所作的皮膚切片,顯示在真皮層 中有排列成聯結索狀及島狀的類基底細胞聚集。這些聚集的類基底細胞包埋在細胞性基質 中,某些區域並呈毛球樣結構;另外在頭皮上禿髮併有輕微硬結的區域,其組織病理顯示在 真皮中有類似的類基底細胞島狀結構,且似乎和原來的毛囊皮脂單位相關聯。因此,我們認 為這是一廣泛性毛囊缺陷瘤病例,一種相當罕見,且經常合併出現自體免疫異常的疾病。 |
英文摘要 | A 60-year-old Taiwanese women with a 7-year history of systemic lupus erythematosus presented with infiltrative papules and plaques on her face and ears for 6 months, and progressive loss of the scalp, eyebrow, axillary, and public hairs and lower eyelashes for 6 years. Histologic sections taken from the right nasolabial fold and right ear demonstrated anastomosing cords and islands of basaloid cells in the dermis embedded in a cellular stroma, and some hair bulb-like structures were noted in the tumor islands. The histopathological findings of the hairless, mildly indurated scaple demonstrated similar islands of ba cells in the dermis, which appeared to be related to the pilosebaceous follicles. Therefore we made the diagnosis of generalized hair follicle hamartoma, a very rare condition usually associated with autoimmune diseases. |
本系統中英文摘要資訊取自各篇刊載內容。