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題 名 | Basaloid Follicular Hamartoma=基底樣毛囊缺陷瘤 |
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作 者 | 廖國棟; 全鳴鐸; 游鴻儒; 彭曄; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 17:2 1999.06[民88.06] |
頁 次 | 頁165-171 |
分類號 | 415.763 |
關鍵詞 | 基底樣毛囊缺陷瘤; Basaloid follicular hamartoma; Hair follicle hamartoma; |
語 文 | 英文(English) |
中文摘要 | 基底樣毛囊缺陷瘤為一稀少之疾病,以明顯特有之組織病理學變化為特徵,但其 臨床表現呈多樣化。吾人報告一29歲女性病患,出生數月後,於其右側大腿後側,經膝外 側,小腿前側,至足背及足內側,出現線狀棕色丘疹及斑塊,合併青春期發生之右腿畸形。 皮膚病灶之組織病理學變化為典型之基底樣毛囊缺陷瘤。此乃第一例合併骨骼畸形發生之基 底樣毛囊缺陷瘤之案例。 |
英文摘要 | Basaloid follicular hamartoma is a rare disease. which is characterized by a distinct histopathologic pattern and in a wide range of clinical presentations. We report a 29-year-old female with linear brownish papules and macules over the right thigh. Lower leg and foot which developed several months after birth. Deformity of the right leg was also noted during puberty. Histopathologic examination of the skin lesions revealed typical findings of basaloid follicular hamartoma. This is the first case of basaloid follicular hamartoma associated with bony abnormality. |
本系統中英文摘要資訊取自各篇刊載內容。