頁籤選單縮合
題 名 | Purpura Fulminans in Children: Report of Two Cases=兒童猛爆型紫斑:二病例報告 |
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作 者 | 黃基家; 江東和; 邱政洵; | 書刊名 | 中華民國小兒科醫學會雜誌 |
卷 期 | 40:2 民88.03-04 |
頁 次 | 頁119-120+141 |
分類號 | 417.5637 |
關鍵詞 | 猛爆型紫斑; 奈瑟氏腦膜炎雙球菌; Purpura fulminans; Neisseria meningitidis; |
語 文 | 英文(English) |
中文摘要 | 猛爆型紫斑為一罕見之表皮出血、肢體壞疽經常伴隨著休克的致死性疾病,腦膜炎雙球菌 造成的敗血症和腦膜炎是其常原因。臨床上因其病程進展迅速,若無及時診斷及治療,病童常常很 快的死亡,第二個病例則是給予立時的抗生素、肝素與輸血治療而得以存活且幾乎無後遺症。我們 認為發病時年紀小且有嚴重的凝血病變的患者容易治死,早期確定診斷與正確治療可以及時挽回生 命。 |
英文摘要 | Purpura fulminans, usually seen in previously healthy children acquiring severe infections, especially meningococcal sepsis and meningitis, is a rare catastrophic disease with initial hemorrhagic skin lesions rapidly progressing to gangrene accompanied by shock and frequently resulting in death. We report 2 cases of purpura fulminans who were diagnosed in the past 2 years. Both blood cultures yielded Neisseria meningitidis. One of them expired within 48 hours after admission despite aggressive therapy. The second patient, who received the treatment of heparin, antibiotics, and blood product replacement, survived with minimal sequelae. We deem young age and severe coagulopathy are especially associated with a fatal outcome in children with purpura fulminans. Early recognition of this disease and prompt appropriate therapy may be lifesaving for these patiemts. |
本系統中英文摘要資訊取自各篇刊載內容。