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題 名 | Adrenal Extramedullary Hematopoietic Tumor in a Patient with β-Thalassemia=發生於乙型海洋性貧血之腎上腺骨髓外造血腫瘤 |
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作 者 | 莊正鏗; 朱聖賢; 方基存; 吳金和; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 97:6 1998.06[民87.06] |
頁 次 | 頁431-433 |
分類號 | 415.513 |
關鍵詞 | 乙型海洋性貧血; 腎上腺骨髓外造血腫瘤; Extramedullary hematopoiesis; β-thalassemia; Adrenal; Myelofibrosis; |
語 文 | 英文(English) |
英文摘要 | We report a case of adrenal extramedullary hematopoiesis in a 27-year-old woman with β-thalassemia. She underwent cholecystectomy for gallstones and splenectomy for splenomegaly at the age of 20 years. In January 1996, she was admitted to our hospital because of a palpable nontender mass in the right subcostal area. Ultrasound, computed tomography, and magnetic resonance imaging disclosed a right suprarenal mass 7.5*5.8 cm in size. Surgical exploration and biopsy confirmed the diagnosis of extramedullary hematopoietic (EMH) tumor. The tumor was left in situ. Subsequent follow-up showed no increase in the size of the tumor and no progression of anemia, The patient remained asymptomatic, and no additional EMH tumor developed. Surgery or radiotherapy should be performed only when EMH tumors cause symptoms, such as during spinal cord compression. Adrenal EMH tumors should be considered in thalassemia patients with an adrenal mass, to avoid unnecessary surgical procedures. |
本系統中英文摘要資訊取自各篇刊載內容。