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題 名 | 乙型海洋性貧血的臨床表徵與放射線學表現的相關性 |
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作 者 | 邱宏仁; | 書刊名 | 中華民國小兒科醫學會雜誌 |
卷 期 | 31:2 民79.03-04 |
頁 次 | 頁97-102 |
分類號 | 415.513 |
關鍵詞 | 乙型海洋性貧血; 臨床表徵; 放射線學表現; |
語 文 | 中文(Chinese) |
中文摘要 | 從民國68年至民國75年,榮民總醫院有68例β型海洋性貧血症,在放射線學上有異常發現者有18例。年齡自8個月大至47歲,平均年齡為13歲,男7女11。β型海洋性貧血一般依基因及貧血程度可分為 l)主型major, 2)中間型intermediate, 3)次型minor三種。不同病型有不同的放射線學表微:如骨質疏鬆,肝脾腫大,骨髓外造血成偽腫瘤狀等。吾人等發現患者的放射線學表微與臨床上的病型有一定程度的關聯,即中間型以上的病人比次型者厲害些。 |
英文摘要 | There were altogether 68 patients sufferred from β-thalassemia in the Veterans General Hospital from 1979 to 1986. However only 18 patients had abnormal roentgenologic findings. They were 7 males and 11 females. Their ages ranged from 8 months to 47 years with an average of 13 years. Clinically β-thalassemia was divided into 3 types: 1) thalasemia major, 2) thalassemia intermediate, 3) thalassemia minor. The osteoporosis, hepatosplenomegaly, and extramedullary hematopoiesis with pseudo-tumor formation. We concluded that the roentgenologic manifestation of the patient was more in patients with major or intermediate type. |
本系統中英文摘要資訊取自各篇刊載內容。