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題 名 | 膽汁滯留及正常嬰兒之血清膽汁酸濃度 |
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作 者 | 黃碧蓮; 趙垂勳; 呂志忠; | 書刊名 | 中華民國小兒科醫學會雜誌 |
卷 期 | 28:1 民76.01-02 |
頁 次 | 頁21-28 |
分類號 | 417.517 |
關鍵詞 | 正常; 血清; 滯留; 酸; 濃度; 嬰兒; 膽汁; |
語 文 | 中文(Chinese) |
中文摘要 | 為了建立國人小孩的血清總膽汁酸正常值,以及評估血清及十二腸液中膽汁酸的測定對新生兒肝炎及膽道閉鎖的鑑別診斷價值,本研究共收集271個正常血清檢體,以及37名黃疸嬰兒的血清及十二指腸液,以酵素比色法測定膽汁酸,37名黃疸嬰兒的最後診斷為:新生兒肝炎27名,膽道閉鎖10名,研究結果如下:平均血清總膽汁酸值在母血及配對臍帶血中分別為5.2±3.6μmol/l及6.5±3.6μmol/l,兩值相近,在出生後第一星期為9.2±5.1μmol/l,二至四星期達到最高值15.5±5.8μmol/l,一至三個月時,10.8±4.6μmol/l,以後隨年齡逐漸下降,約一至三歲時趨近於正常成人值4.7±2.5μmol/l,顯示新生兒及嬰兒早期有高膽汁酸血症。新生兒肝炎的平均總膽汁酸值為145.6±67.4μmol/l,膽道閉鎖為210.1±53.9μmol/l,後者比前者27名高(P<0.02),但兩者的膽汁酸多相互重疊,無法用來鑑別診斷。新生兒肝炎中的21名其十二指腸液中有膽汁酸存在,9名(9/10)膽道閉鎖的十二指腸液中無法測得膽汁酸,以十二指腸液膽汁酸之有無來區分兩者,其診斷正確率為82%,為一有用的鑒別診斷方法。 |
英文摘要 | To establish the normal values in children and to evaluate the role of bile acids for differential diagnosis between neonatal heatits and biliary atresia, bile acids levels were measured by enzymatic colorimetric method. The sera and duodenal aspirates from 37 jaundiced infants (27 neonatal hepatitis and 10 biliary atresia), and 271 fasting sera of normal subjects were studied. The results showed: (1) In the first week of age, mean value of serum total bile acids is 9.2±5.1μmol/l. It increases rapidly with the highest level (15.5±5.8μmol/l) in 2 to 4 weeks, then decreases gradually and approaches to the adult level around 1 to 3 years of age. (2) The mean values of serum total bile acids are 145.6±67.4μmol/l in neonatal hepatitis, and 210.1±53.9μmol/l in biliary atresia. Though the value is significantly higher in biliary atresia, it provides little contribution to the differential diagnosis. (3) Bile acids can be detected from duodenal aspirates in 21 out of 27 cases of neonatal hepatitis, while only one case of biliary atresia has traceable level. Using the criteria of presence of bile acids in duodenal aspirates to exclude biliary atresia, the accuracy of diagnosis is 82%. |
本系統中英文摘要資訊取自各篇刊載內容。