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題 名 | 蛋白質流失腸病變及其處置用藥介紹=The Introduction and Medication Management of Protein-losing Enteropathy |
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作 者 | 巫櫻桃; 蕭如君; 許凱倫; 李建瑩; | 書刊名 | 藥學雜誌 |
卷 期 | 31:3=124 2015.09[民104.09] |
頁 次 | 頁32-37 |
分類號 | 415.47 |
關鍵詞 | 蛋白質流失腸病變; 低白蛋白血症; 水腫; Protein-losing enteropathy; PLE; Hypoalbuminemia; Edema; |
語 文 | 中文(Chinese) |
中文摘要 | 蛋白質流失腸病變 (protein-losing enteropathy, PLE) 的特色為血清中蛋白質經 由腸道過度流失,臨床表現為出現低蛋白血症 (hypoproteinemia)、低白蛋白血症 (hypoalbuminemia)、水腫、吸收不良、體重減輕、電解質失衡,甚至可能出現腹水 (ascites)、肋膜積液 (pleural effusion) 或心包膜積液 (pericardial effusion) 等症狀。有許 多原因可能引起 PLE,大多不引起臨床嚴重症狀,但當中以原發性小腸淋巴管擴張症 (primary intestinal lymphangiectasia)、自體免疫疾病、先天性心臟病術後等原因所導致 的 PLE,常伴隨極高的死亡率。近年來雖然 PLE 的治療有進一步的改善,但仍是臨 床很難治療的疾病,盼透過臨床治療成功的案例提供予 PLE 處置參考,以幫助改善 病人預後。 |
英文摘要 | The main clinical feature of protein-losing enteropathy (PLE) is primarily characterized by excessive leakage of serum proteins into the gastrointestinal tract, resulting in common clinical manifestations such as hypoproteinemia, hypoalbuminemia, edema, malabsorption, 第31卷第3期 Sep. 30 2015 藥學雜誌 第124冊37 藥 物 科 學 body weight loss and electrolyte imbalance. In some rare cases, symptoms such as ascites, pleural effusion or pericardial effusion may even appear. There are many factors those might cause PLE, but most patients do not show serious clinical signs. However, for persons having primary intestinal lymphangiectasia, autoimmune disease or post-operation congenital heart disease leading to PLE, high mortality rate is frequently observed. Although the treatment of PLE has advanced greatly in recent years, this disease is still difficult to treat. Several successful clinical cases from the past can help us provide better care in managing patients with PLE. |
本系統中英文摘要資訊取自各篇刊載內容。