頁籤選單縮合
題 名 | Acute Hemorrhagic Edema of Infancy=小兒急性出血性水腫 |
---|---|
作 者 | 楊志勛; 施一新; 楊麗珍; 曾興隆; 郭承統; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 16:3 1998.09[民87.09] |
頁 次 | 頁236-241 |
分類號 | 415.74 |
關鍵詞 | 小兒急性出血性水腫; Acute hemorrhagic edema of infancy; Leukocytoclastic vasculitis; |
語 文 | 英文(English) |
中文摘要 | 小兒急性出血性水腫( acute hemorrhagic edema of infancy )是一罕見之白 血球脆裂性血管炎的變異型。其臨床表現相當急速,但是短暫的病程後會自然痊癒。臨床表 現為疼痛出血點或瘀斑,並快速轉為標靶狀腫脹感的紅斑,頭部及四肢末端是好發部位, 血 管炎僅局限於皮膚,痊癒後不會有留下其他後遺症。本文報告一例七月大男嬰於雙耳雙頰及 四肢出現腫脹環形紅斑,皮膚切片呈現血管類纖維化壞死及栓塞,病患在服用抗組織氨及類 固醇十日後皮疹完全消失,追蹤觀察二年至今病患仍相當健康,且無復發之現象。 |
英文摘要 | Acute hemorrhagic edema of infancy is an unusual variant form of leukocytoclastic vasculitis. The clinical picture has a sudden onset with a short benign course followed by spontaneous recovery. It presents clinically as painful petechiae and ecchymosis that become edematous and develop a target-like (cockade) appearance. The head and distal portions of the extremities are favored sites. The vasculitis appears to be limited to the skin, and complete recovery without sequelae is expected. We report a case of 7-month-old boy with one day history of redness, tenderness, and swelling of bilateral ears and cheeks and hemorrhagic lesions on the thighs, forearms. Skin biopsy revealed fibrinoid necrosis and thrombosis of vessels. These skin lesions cleared completely in 10 days after treatment with oral anti-histamine and prednisolone. The child remained healthy and no recurrence was noted during the following 2 years. |
本系統中英文摘要資訊取自各篇刊載內容。