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題 名 | Transition from Pemphigus Vulgaris to Pemphigus Foliaceus--Report of Two Cases=尋常性天疱瘡轉換至落葉性天疱瘡--兩個病例報告 |
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作 者 | 石博宇; 郭承統; 邱健群; 王佳茹; 游可任; 何信君; 洪宏翔; 官裕宗; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 27:1 2009.03[民98.03] |
頁 次 | 頁52-58 |
分類號 | 415.765 |
關鍵詞 | 尋常性天疱瘡; 落葉性天疱瘡; Pemphigus; Desmoglein; Subtype transition; Epitope spreading; |
語 文 | 英文(English) |
英文摘要 | Pemphigus vulgaris (PV) and pemphigus foliaceus (PF) are two different subtypes of the pemphigus group with distinct clinicopathologic features. Clinically, PV presents with mucosal, mucocutaneous, or cutaneous lesions whereas PF lesions are primarily cutaneous. Histopathologically, intraepidermal acantholysis is located at the granular layer in PF and suprabasally in PV. Traditionally, these differences are used for basis of treatment selection and prognostic estimation. However, infrequent transition between the subtypes has been reported. Herein we describe two cases of PV with transition into PF and discuss the proposed mechanism for this phenomenon. |
本系統中英文摘要資訊取自各篇刊載內容。