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題 名 | Huge Solitary Fibrous Tumor of the Pleura--Report of a Case=巨大肋膜腔單發性纖維瘤--單一病例報告 |
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作 者 | 黃俊凱; 吳惠東; 余忠仁; | 書刊名 | 胸腔醫學 |
卷 期 | 28:2 2013.04[民102.04] |
頁 次 | 頁131-137 |
分類號 | 415.43 |
關鍵詞 | 單發性纖維瘤; 肋膜腔腫瘤; 預後; Solitary fibrous tumor; Pleural tumor; Prognosis; |
語 文 | 英文(English) |
中文摘要 | 肋膜腔單發性纖維瘤是一種罕見的間質細胞腫瘤。它通常是無症狀的並常常在診斷前成長為一個巨大的腫瘤。有10至20%的肋膜腔單發性纖維瘤被診斷為惡性腫瘤。在完整的手術切除下,良性肋膜腔單發性纖維瘤是可以治癒的。臨床和影像學評估對於肋膜腔單發性纖維瘤的診斷可以有一定的幫助,但往往無法獲得明確的診斷。例行的細針穿刺活檢不建議用於肋膜腔單發性纖維瘤的診斷,這是由於診斷率低和可能的穿刺路徑上的轉移。然而,如果病理的結果將影響後續的治療或當手術是禁忌症時,病理組織切片仍是必要的。在此,我們報告一位79歲的婦女有漸進性呼吸困難的症狀,並在左下肺區發現巨大腫塊。病人及其家屬決定不接受手術治療。經由超音波指引的細針穿刺活檢,她被診斷出肋膜腔單發性纖維瘤。 |
英文摘要 | Solitary fibrous tumor of the pleura (SFTP) is a rare neoplasm from mesenchymal cells. It is usually asymptomatic and the diagnosis is often delayed; 10-20% of SFTPs are classified as malignant. Benign SFTPs are almost curable with complete surgical resection. Clinical and radiological assessment can provide a hint of SFTP, but is often inadequate for a definitive diagnosis. Although routine fine needle aspiration biopsy (FNAB) is not suggested in SFTP, tissue proof is still necessary if disease management would be substantially affected by the results, or if surgical intervention is contraindicated. Herein, we report a 79-year-old woman with progressive dyspnea and a huge mass in the left lower lung zone. She and her family decided against surgical intervention. She was diagnosed as having SFTP with echo-guided FNAB. |
本系統中英文摘要資訊取自各篇刊載內容。