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題 名 | Acute Respiratory Distress Syndrome Associated with Rabies: A Case Report=狂犬病合併急性呼吸迫窘症候群一病例報告 |
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作 者 | 許永祥; 卓麗貞; 王立信; 陳立光; 李仁智; 楊惠華; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 22:2 民95.02 |
頁 次 | 頁94-98 |
分類號 | 415.239 |
關鍵詞 | 狂犬病; 急性呼吸迫窘症候群; 誘發一氧化氮合成酵素; Rabies; Acute respiratory distress syndrome; ARDS; Inducible nitric oxide synthase; iNOS; |
語 文 | 英文(English) |
中文摘要 | 狂犬病合併急性呼吸迫窘症候群是最常見致命的併發症,雖然發生機率不高。我們報告一例 45 歲女性由湖南境外移入的狂犬病。她被家犬咬過後第 61 天發現四肢麻痺的神經症狀和恐水症,臨床病程漸近發展成高燒、腦炎、急性呼吸迫窘症候群,於 12 天後往生。病理解剖証明狂犬病腦炎侵犯延髓、視丘、一部份橋腦、小腦和海馬迴。肺臟病理表現為機化期急性呼吸迫窘症候群包括擴散性肺泡損傷,透明膜形成,第二型肺泡細胞增生,伴隨纖維母細胞增生和單核球浸潤肺間質、免疫組織化學染色及聚合酵素連鎖反應並無法偵測到狂犬病毒。同時免疫組織化學染色發現肺泡巨噬細胞有很強的誘發一氧化氮合成酵素 (iNOS) 表達。免疫機制合併誘發一氧化氮合成酵素 (iNOS) 表達,而無發現狂犬病毒直接侵襲肺臟,可能參與狂犬病有關的急性呼吸迫窘症候群。 |
英文摘要 | Acute respiratory distress syndrome (ARDS) is the first potentially lethal complication in rabies virus infection, although its occurrence is rare. We report on a fatal case of rabies virus infection in a 45-year-old woman from Hu-Nan Province, China. The neurologic signs of limb numbness and water phobia occurred from 61 days after the dog bite; the clinical course was progressive, with the most severe clinical manifestations being fever, encephalitis, and ARDS. The woman expired 12 days after admission to the hospital. An autopsy proved rabies encephalitis, mainly involving the medulla oblongata, the thalamus, part of the pons, the cerebellum, and the hippocampus. The lung pathologic examination revealed the organizing phase of ARDS with diffuse alveolar damage, hyaline membrane formation, type II alveolar cell hyperplasia accompanied by proliferation of fibroblasts and infiltration of mononuclear cells into the interstitial space. Immunohistochemistry stain and reverse transcription-polymerase chain reaction for rabies virus failed to demonstrate the organism in the lung tissue. Strong expression of inducible nitric oxide synthase (iNOS) was detected in the alveolar macrophages. An immunologic mechanism with iNOS expression in the absence of direct invasion of the organism may participate in the pathogenesis of ARDS associated with rabies. |
本系統中英文摘要資訊取自各篇刊載內容。