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頁籤選單縮合
題 名 | Retrocaval Ureter: Report of Two Cases and Literature Review=下腔靜脈後輸尿管--二病例報告及文獻回顧 |
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作 者 | 林鴻裕; 周以和; 黃書彬; 李永進; 蔡秀男; 鄭皓碩; 黃俊雄; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 19:3 2003.03[民92.03] |
頁 次 | 頁127-131 |
分類號 | 416.274 |
關鍵詞 | 下腔靜脈後輸尿管; 電腦斷層; 核磁共振; Retrocaval ureter; Computerized tomography; MRI; |
語 文 | 英文(English) |
中文摘要 | 下腔靜脈後輸尿管為比較罕見之先天性異常,意指輸尿管跑到下腔靜脈後並被下腔靜脈壓迫。導因為下腔靜脈的異常胚胎發展結果導致在腰部的右側心下靜脈未萎縮。在此,本文報導二例下腔靜脈後輸尿管並回顧相關的文獻。個案一為 7 歲男孩有右腰疼痛,另一個案為 40 歲男性於身體檢查時,經超音波意外發現有右腎水腫。此二案例皆接受逆行性輸尿管腎盂攝影,並顯示出典型的 S 型態;再由電腦斷層和核磁共振確定為下腔靜脈後輸尿管。更進一步,個案經由輸尿管輸尿管重接手術,其組織病理的特徵顯示一位患者之輸尿管有局部鱗狀細胞化生,另一位則有慢性發炎和纖維化。術後追蹤顯示,水腫和腎功能皆有改善。下腔靜脈後輸尿管是少見的疾病,而手術通常是有療效的。 |
英文摘要 | Retrocaval ureter is a rare congenital anomaly in which the ureter passes behind, and is compressed by, the inferior vena cava. Its etiology is assumed to be abnormal embryologic development of the inferior vena cava as a result of atrophy failure of the right subcardinal vein in the lumbar portion. We report two cases of retrocaval ureter and review the relevant literature. One patient was a 7-year-old boy who presented with right flank pain. The other was a 40-year-old male who was found to have right hydronephrosis accidentally on abdominal sonography during a health examination. Both underwent retrograde pyelography which showed the typical S-shape of a retrocaval ureter. Abdominal computerized tomography and magnetic resonance imaging confirmed the diagnosis of retrocaval ureter. Ureteroureterostomies were performed. One patient showed focal squamous metaplasia of the ureter and the other had chronic inflammation and fibrosis. Follow-up studies showed improvement in hydronephrosis and renal function in both patients. We conclude that retrocaval ureter is a rare disorder and surgical correction is usually effective. |
本系統中英文摘要資訊取自各篇刊載內容。