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題 名 | Puberty and Clinical Course of Immunoglobulin a Nephropathy in Children=青春期與兒童甲型免疫球蛋白腎病的臨床病程 |
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作 者 | 李宜燕; 林清淵; | 書刊名 | 臺灣腎臟醫學會雜誌 |
卷 期 | 15:1 2001.03[民90.03] |
頁 次 | 頁3-8+34 |
分類號 | 417.574 |
關鍵詞 | 甲型免疫球蛋白腎病; 青春期; 年齡相關; 性別; IgA nephropathy; Puberty; Age-related; Gender; Sex hormones; |
語 文 | 英文(English) |
中文摘要 | 兒童甲型免疫球蛋白質腎病比成人有較好的預後。在動物和臨床實驗中,男性在慢性腎病的病程進展較快,而這其中的原因尚未有明確的定論。因此我們回溯探討由1997年至2000年共一百二十例發病牛齡小於十八歲且一直在門診追蹤的甲型免疫球蛋白腎病的病童,將其分為兩組:小於十三歲和大於等於十三歲;追蹤他們的預後、臨床表現包括血尿、蛋白尿、血壓、腎功能和病理變化,結果發現早期發病的病童中,男性有較多的嚴重蛋白尿;而大於等於十三歲發病的病童,嚴重蛋白尿以女性居多。女性或病理表現是腎絲球微小變化的病童較易緩解;若病理表現是腎絲球微小變化的病童,在青春期前均會改善,則持續蛋白尿和血尿的比例較高。追蹤期間沒有病童進行到未期腎。以上結果顯示,青春期前和青春期間的病童,在甲型免疫球蛋白腎病的較好的預後,性荷爾蒙可能對賢臟的預後有影響。 |
英文摘要 | IgA nephropathy is a progressive disease in adult patients. Amore benign prognosis has been found in children. In various experimental models of renal injury, the rate of progression of renal disease is influenced by gender. Male gender is associated with a more rapid progression of chronic renal disease in adults. The reasons for the age-related differences in the natural history of IgA nephropathy in children have yet been elucidated. And the relationships between puberty and IgA nephropathy are also unknown. To investigate differences between the children with regard to gender, age of onset (before and during puberty period), and pathologic findings of IgA nephropathy in children. From 1979 to 2000, the clinical presentation, renal biopsy findings, and subsequent clinical course of IgA nephropathy were studied retrospectively in 120children under 18 years old. Also clinical and pathologic findings in those less than 13 and those older than 12 years old at onset were compared. Sixty patients were 12 years of age or younger (group I ) and 60 were 13 years of age or older (group II) at onset. All patients were less than 18 years of age at onset. There were different between gender and the age of onset in patients with heavy proteinuria. The incidence of heavy proteinuria was greater in males in the early onset group. But in the late onset group, the incidence of heavy proteinuria was greater in females. The clinical remission rate was better in those female patients and the pathologic findings of the first biopsy specimen showed minimal glomerular change. The incidence of subsequent renal failure, persistent proteinuria and heavy hematuria was greater in the pathologic findings of masangial proliferation or masngial sclerosis. The patients with grade I pathological finding improved before puberty. No children developed ESRD during the follow up period. The disease followed a more benign course in children. These observations suggest some puberty-related differences in the natural history of childhood IgA nephropathy. The prepuberty and puberty period children with IgA nephropathy have a more benign course. This finding is comparable to effects of the sex hormones that influence much of the pathogenesis of renal disease progression. |
本系統中英文摘要資訊取自各篇刊載內容。