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題 名 | Ankylosing Spondylitis with Severe Chondrocalcinosis: Case Report=僵直性脊椎炎合併嚴重軟骨鈣化:病例報告 |
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作 者 | 何輝煌; 楊文一; 羅淑芬; | 書刊名 | 長庚醫學 |
卷 期 | 22:3 1999.09[民88.09] |
頁 次 | 頁536-540 |
分類號 | 415.695 |
關鍵詞 | 軟骨鈣化; 僵直性脊椎炎; 關節炎; 關節傷害與修復; Chondrocalcinosis; Ankylosing spondylitis; Arthritis; Joint damage and repair; |
語 文 | 英文(English) |
中文摘要 | 軟骨鈣化(Chondrocalcinosis)為發生於纖維軟骨或透明軟骨之焦磷酸鈣晶體沈積病 變,事實上,除了關節軟骨以外,焦磷酸鈣晶體亦可沈積於肌腱、韌帶,關節囊及關節滑膜。 晶體由沈積處剝落進入關節滑膜液,引發白血球吞噬可以引起急性關節炎,此即為假性痛風 發作,除了急性關節炎以外有些病患則以亞急性或慢性關節炎來表現,亦可以只有軟骨鈣化 而任何臨床症狀。軟骨鈣化以發生於老年人為主,若發生於60歲以下病患則多合併新陳代 謝疾病(如副甲狀腺機能亢進症、血色素沈積症等)或為家族性之軟骨鈣化病。本文報告一42 歲僵直性脊椎炎女性病變合併多處關節嚴重軟骨鈣化,其軟骨鈣化病因不明,推測可能與關 節炎引起之軟骨傷害與修復過程引起焦磷酸鈣晶體沈積有關。 |
英文摘要 | The term chondrocalcinosis is often used to describe the radiological or pathological features of calcified joint cartilage, and it usually indicates the deposition in cartilage of calcium pyrophosphate dihydrate. The prevalence of chondrocalcinosis increases with age, with dramatic increases occurring in the decades past age 60. In younger patients with chondrocalcinosis, either clinical evidence of associated metabolic diseases leading to the chondrocalcinosis or familial disease occurrence usually can be detected. We report a 42-year-old Chinese woman with ankylosing spondylitis and arthritis involving multiple peripheral joints. Severe chondrocalcinosis was detected incidentally in this patient, however, subsequent studies revealed no associated metabolic disease or familial susceptibility and the clinical features of this patient were different from those of ankylosing chondrocalcinosis (pseudoankylosing spondylitis). The cause of chondrocalcinosis in this patient remains unknown, but joint damage and repair could have been initiating or aggravating factors of the chondrocalcinosis. |
本系統中英文摘要資訊取自各篇刊載內容。