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題 名 | Prolonged Survival of Patient with Recurrent Pulmonary Metastasis from a Primary Adrenal Cortical Carcinoma--A Case Report=長期存活之原發性腎上腺癌合併肺轉移--病例報 |
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作 者 | 陳寶瓊; 王朝弘; 林清基; 詹錕鋙; | 書刊名 | 胸腔醫學 |
卷 期 | 13:1 1998.03[民87.03] |
頁 次 | 頁27-33 |
分類號 | 415.818 |
關鍵詞 | 腎上腺癌; 復發性轉移; 長期存活; Adrenal cortical carcinoma; Recurrent metastasis; Prolonged survival; |
語 文 | 英文(English) |
中文摘要 | 腎上腺癌是一種很少見但高度惡性的腫瘤,死亡率很高,而年的存活率是22-31% ;而平均存活的時間是十四個月。現在我們要報一個特殊腎上腺癌的病例。此病人十八年前 曾因腎上腺良性腫瘤開過刀,但於開刀九年後發現有腎上腺癌併肺轉移。那時候病人以庫欣 症候群及肺部症狀來表現,經診斷有腎上腺癌細胞轉移到肺部,因此病人接受外科手術治療 。六年之後,因復發肺部轉移而做左肺切除。手術後再過三年發現腎上腺癌復發,而發現淋 巴腺,肺及胸骨有癌細胞轉移。此次病人拒絕開刀,願意接受內科治療。 目前此病人病情穩定,我們現在來討論各種影響腎上腺癌存活的因素。早期腎上腺腫瘤切除 可說是影響病人存活的因素。病人因發現肺轉移及復發性的腎上腺腫瘤經證明當時良性腎上 腺腫瘤實為惡性腎上腺癌。因此我們的結論是早期發現及早期外科手術治療是影響腎上腺癌 存活率的兩個最重要因素。 |
英文摘要 | Adrenal cortical carcinoma is a rare but highly malignant tumor. Mortality rate is high and the five-year survival is 22 to 31% with median survival time of 14 months. We now report a remarkable case of an adrenocortical carcinoma surviving 18 years after surgical removal of an adrenal tumor and 9 years after pulmonary metastasis from a primary adrenocortical carcinoma. Pulmonary symptoms and Cushing's syndrome presented 9 years after removal of a left adrenal tumor. There was pathological proof of pulmonary metastasis from a primary adrenocortical carcinoma. Six years after lobectomy and resection of a recurrent left adrenal tumor, there was recurrent pulmonary metastasis for which lung resection was done. Three years later, there was recurrence of left adrenal tumor with retroperitoneal lymph nodes, lung and sternal bone metastases. Patient refused surgery so was only given medical treatment and has remained in stable condition. We discussed factors affecting survival of adrenocortical carcinoma. Early resection of the adrenal tumor 18 years ago in this patient might have contributed to a long-term survival. Presence of pulmonary metastasis and adrenal carcinoma over the previous site of adrenal tumor proved that the previously resected tumor was in fact an adrenal carcinoma. We conclude that early diagnosis and surgery are the two most important factors affecting survival of adrenal cortical carcinoma. |
本系統中英文摘要資訊取自各篇刊載內容。