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題 名 | 中鏈脂肪酸油飲食對兒童頑固性癲癇之臨床經驗 |
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作 者 | 萬居仁; 遲景上; 麥淑珍; | 書刊名 | 中華民國營養學會雜誌 |
卷 期 | 19:2 1994.04[民83.04] |
頁 次 | 頁159-172 |
分類號 | 417.5845 |
關鍵詞 | 中鏈脂肪酸油; 生酮飲食; 頑固性癲癇; 酮體; Mct oil; Ketogenic diet; Refractory epilepsy; Ketone body; |
語 文 | 中文(Chinese) |
中文摘要 | 作者於民國76年,在台中榮民總醫院營養室與小兒神經科醫師合作,針對經醫師高度選擇之兒童癲癇患者,於住院期間給予中鏈脂肪酸油之生酮飲食(MCT oil ketogenic diet)來控制其癲癇之發作。共計有13名頑固性癲癇患童,其中男6名,女7名,年齡2-10歲。這些癲癇患童之發作型態包括:失運動-矢張力癲癇發作(Akinetic-Atonic seizures)5位,Lennox-Gastaut syndrome4位,嬰兒點頭痙攣(Infantile spasms)2位,複雜性局部癲癇發作(Complex partialseizures)1位,局部癲癇發作(Simple partial seizures)1位,他(她)們均來自台中榮民總醫院小兒神經科門診,每位患童均有一份小兒癲癇記錄表及食物治療記錄表。所有患童入院後先禁食,每位患童在其食物治療記錄表上記錄每日血糖、血酮、脈博、呼吸、血壓、體重、發作次數和臨床發作型態,並每日檢查尿及血液中之酮體(ketone bodies),直到尿或血中酮體出現後即給予生酮飲食。住院期間臨床上癲癇發作次數之改善有2例達80以上之改善,6例呈60-80改善,4例呈10-60之改善,1例患童毫無改善。抗癲癇藥物之種類及藥量均有減少,但沒有一位患童能完全停止用藥。唯因大多數患童出院後家長未能配合確實繼續給予此種治療飲食,以致無法評估其長期療效及對於行為、記憶及學習之影響。 |
英文摘要 | A co-operative study between the Dietary Department and Pediatric Department to select children with refractory epilepsy using medium-chain triglycerideoil (MCT oil) ketogenic diet was performed prospectively during 1987 in TaichungVeterans General Hospital. Thirteen patients, 6 bodys and 7 girls, aged from 2to 10 years were chosen as participants. Their seizure patterns included: akineticatonic seizure,5; Lennox-Gastaut syndrome, 4; infantile spasms, 2; complex partialseizure, 1; simple partial seizure, 1. Clinical examination and dietary intake wererecorded in detail on a chart in the course of therapy in hospital. They wereall put on absolute NPO (nothing by mouth) status after admission, daily routinerecord on blood glucose, ketone bodies, pulse rate, body weight, respiratory rate, frequency and pattern of seizure was kept; urine screening for ketone bodies wasperformed daily and ketogenic diet was given as soon as a result of positiveketone bodies was found in the urine and blood. As a result, during hospitalization, 2 patients had a 80 improvement, 6 patients got 60-80. and 4 patientsgot 10-60 improvement, one had no response at all. Usual dosage for anticonvulsant was decreased to various degree, however, as most of the families could not keep on using the MCT oil ketogenic diet at home, so long-term evaluation ofthe diet therapy on seizure control, behaviour, memory and learning ability failedto evaluate. |
本系統中英文摘要資訊取自各篇刊載內容。