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題 名 | 地中海型貧血病患血鐵沈積現象於磁振造影之臨床表現=Iron Deposition Clinical Performance of Magnetic Resonance Imaging in Patients with Thalassaemia |
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作 者 | 陳霆霖; 陳素秋; 楊斐適; 莊奇容; | 書刊名 | 中華放射線技術學雜誌 |
卷 期 | 40:2 2016.06[民105.06] |
頁 次 | 頁90-96 |
分類號 | 415.513 |
關鍵詞 | 地中海型貧血; 血鐵沈積症; 生物檢測; 磁振造影; Thalassaemia; Hemochromatosis; Bio-examination; Magnetic resonance image; |
語 文 | 中文(Chinese) |
中文摘要 | 地中海型貧血病患因長期輸血之故,通常都伴隨著血鐵沈積症,會對體內器官造成不可逆之傷害,但目前病患體內鐵質沈積含量的檢查大都仰賴血液檢查,無法經由非侵入性方式量化體內單一器官之鐵質沈積量。然而,磁振造影(magnetic resonance imaging, MRI)除了具有非侵入性及無輻射線的優點之外,對於體內單一器官之鐵質沈積量還具有量化之功能。故本回溯性研究收集了三十二名此類病患之磁振影像的T2*和肝臟鐵質含量(liver iron concentration, LIC)等資料共九十三筆,進行心臟及肝臟之鐵質沈積量評估,同時與血清載鐵蛋白(ferritin)、血紅素(hemoglobin)等生物檢測數據,進行相關性之統計分析。結果顯示T2*_(肝臟)/LIC(r=-0.647, p<0.001)及T2*_(肝臟)/ferritin(r=-0.521, p<0.001)兩組在統計上呈現極顯著中度負相關性,而LIC/ferritin(r=0.465, p<0.001)則呈現極顯著中度正相關性;因此,肝臟之鐵質沈積量確實可藉由ferritin 及MRI 參數(T2*和LIC)來呈現。至於心臟方面,T2*_(心臟)/LIC(r=-0.207, p=0.047)的顯著負相關性說明了LIC值可以當作心臟有過量鐵質沈積的指標。最後,hemoglobin/ferritin 為顯著相關性(r=0.204,p=0.050),則意味著具有高ferritin 者並不易產生貧血。目前國內鮮少醫學中心或區域醫療院所利用磁振造影技術針對此類患者評估體內單一器官之鐵質沈積量,希望我們的研究結果可提供臨床上診療之參考。 |
英文摘要 | Due to long-term blood transfusions, thalassemia patients usually accompanied with hemochromatosis. Overload of iron deposition always caused irreversible damage of organs inside human body; therefore it is getting more and more important for iron deposition assessment of single organ in vivo. The iron concentration determinations in vivo generally rely on bio-examination; in addition, the iron deposition of single organ is nearly unable to be quantified via non-invasive method in clinical routine. However, magnetic resonance imaging (MRI) method not only has the advantages of non-invasive and no radiation, but also possesses the iron deposition quantification ability of single organ. In this retrospective research, the magnetic resonance imaging data, T2* and liver iron concentration (LIC), from thirty-two thalassaemia patients were collected. After that, the iron deposition amount in their heart and liver were evaluated and the correlation analyses were performed as well as the bio-examination data (ferritin and hemoglobin). According to the results, a highly negative correlation were observed on T2*_(liver)/ferritin (r=-0.521, p<0.001) and T2*_(liver)/LIC (r=-0.647, p<0.001), in addition, it existed highly positive correlation between LIC and ferritin (r=0.465, p<0.001). Therefore, hepatic iron overload could be assessed by serum biochemical markers and MRI measurements. By the way, the result of T2*_(heart)/LIC (r=-0.207, p=0.047) indicated that LIC may serve as the reference for heart iron overload. Finally, the significant correlation between ferritin and hemoglobin (r=0.204, p=0.050) told us those patients with higher ferritin may not have anemia. In Taiwan, there are rare medical centers or local hospitals used magnetic resonance imaging technique to assess the content of iron deposition for single organ in vivo at present. We wish this research could benefit further clinical research strategy as well as the diagnosis and patient treatment. |
本系統中英文摘要資訊取自各篇刊載內容。