頁籤選單縮合
題 名 | Primary Bone Diffuse Large B Cell Lymphoma with Initial Presentation of IgM Monoclonal Gammopathy, Cold Agglutinin Disease=以IgM單株免疫球蛋白,冷凝集素症為表現之原發性骨瀰漫性大B細胞淋巴瘤 |
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作 者 | 張景明; 滕傑林; 古凡宸; 黃文豊; | 書刊名 | 臺灣癌症醫學雜誌 |
卷 期 | 29:1 2013.03[民102.03] |
頁 次 | 頁34-40 |
分類號 | 415.6 |
關鍵詞 | 原發性骨淋巴瘤; 單株免疫球蛋白; 冷凝集素症; Primary bone lymphoma; Monoclonal gammopathy; Cold agglutinin disease; |
語 文 | 英文(English) |
中文摘要 | 原發性骨淋巴瘤為罕見的疾病,佔所有非何杰金氏淋巴瘤不到 1%,組織學型態以瀰 漫性大 B 細胞淋巴瘤為最常見。我們報告的病例是一位 61 歲男性,首先表現有 IgM 單株 免疫球蛋白及冷凝集素症,最終診斷為原發性骨瀰漫性大 B 細胞淋巴瘤。這位病人在門 診追蹤 IgM 單株免疫球蛋白及冷凝集素症,直到十個月之後,病人開始出現多處骨頭疼痛、下背痛。腰椎核磁共振檢查發現腰椎壓迫性骨折,且有脊椎周邊軟組織病灶;切片 報告為瀰漫性大 B 細胞淋巴瘤。正子攝影發現全身唯有多處骨頭顯影,故診斷為原發性 骨淋巴瘤。病人接受針對腰椎的放射線治療以獲得症狀緩解,接續 3 次的 R-CHOP 化學 治療,得到部分反應,此病人目前正在治療中。 |
英文摘要 | Primary bone lymphoma is a rare clinical entity accounting for less than 1% of all non-Hodgkin’s lymphoma. Diffuse large B cell lymphoma (DLBCL) was the most common histologic subtype in primary bone lymphoma. Here we reported a 61-year-old man who was eventually diagnosed as primary bone DLBCL with initial presentation of IgM monoclonal gammopathy and cold agglutinin disease (CAD). This patient regularly followed up his IgM monoclonal gammopathy and CAD until he suffered from multiple bone and lower back pain 10 months after the initial diagnosis. Magnetic resonance imaging revealed lumbar spine compression fracture with paraspinal soft tissue mass. Lumbar spine biopsy proved the diagnosis of DLBCL. Positron emission tomography displayed multiple osseous tissue uptake, which is consistent with primary bone lymphoma. He received radiotherapy to the lesion of lumbar spine for symptom relief. Then 3 cycles of chemotherapy with R-CHOP regimen (rituximab, cyclophosphamide, doxorubicin, vincristine, and prednisolone) was administered and received partial response. He continues to receive treatments with regular follow up. |
本系統中英文摘要資訊取自各篇刊載內容。