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頁籤選單縮合
題 名 | Primary Bone Lymphoma Presenting as Lumbar Radiculopathy=以腰椎坐骨神經病變表現之原發性骨髓淋巴瘤 |
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作 者 | 郭岱宗; 陳功深; 張國明; | 書刊名 | 臺灣癌症醫學雜誌 |
卷 期 | 26:5 2010.10[民99.10] |
頁 次 | 頁205-212 |
分類號 | 415.6 |
關鍵詞 | 原發性骨髓淋巴瘤; 薦椎; 瀰漫性大型B細胞淋巴瘤; 化學治療; Primary bone lymphoma; Sacrum; DLBCL; Chemotherapy; |
語 文 | 英文(English) |
中文摘要 | 原發性骨髓淋巴瘤為一相當少見但又相當明確之臨床病理疾病,且一般認為其係由淋巴以及骨髓造血組織所組成之惡性腫瘤。通常易與其他原發性淋巴瘤或傷害造成混淆。常見之臨床表現包括骨頭疼痛、關節疼痛、骨頭或關節腫脹、以及脊椎神經壓迫等。我們報告一位62歲男性腰薦椎原發性骨髓淋巴瘤之病患其腫瘤壓迫神經,以典型腰椎坐骨神經病變來表現。術後之病理組織檢查確認為瀰漫性大型B細胞淋巴瘤,所以病患接下來接受了完整六個療程的R-CHOP輔助組合性化學治療。持續在門診追蹤至術後33個月皆未發現有復發或者遠處轉移之情況發生。關於脊椎淋巴瘤之資訊實在相當有限,故在這篇文章,我們將關於發生率、臨床表現、放射線特徵、病理診斷及現代治療方針做文獻之回顧及探討。 |
英文摘要 | Primary bone lymphoma (PBL) is an extremely rare and distinct clinicopathological entity that has been recognized as a malignant neoplasm composed of lymphoid and myeloid tissues. It is often confused with other primary site of lymphoma or injuries of bone. The common clinical presentations include bone pain, arthralgia, bone/joint swelling and spinal cord compression. We report a 62-year-old male patient suffering primary lumbosacral lymphoma with epidural extension, who manifested with typical lumbar radiculopathy. Postoperative histopathological investigation revealed a diffuse large B-cell lymphoma (DLBCL), and further adjuvant multi-agent chemotherapy with rituximab, cyclophosphamide, doxorubicin, vincristine and prednisolone (R-CHOP) was prescribed for 6 courses. During follow-up at our outpatient office, no evidence of distant relapse or local recurrence was noted at 33 months postoperatively. There is limited information regarding spine lymphoma. In this article, relevant literature regarding the incidence, presentation, roentgenographic features, pathological diagnosis, and modern treatment strategies is reviewed. |
本系統中英文摘要資訊取自各篇刊載內容。