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題 名 | Growth Hormone Therapy in Neonatal Patients With Methylmalonic Acidemia=生長激素治療於新生兒甲基丙二酸血症的臨床成效 |
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作 者 | 高銓宏; 劉美英; 劉孜孜; 蕭廣仁; 鄭康祥; 黃天宏; 林祥宇; 牛道明; | 書刊名 | Journal of the Chinese Medical Association |
卷 期 | 72:9 2009.09[民98.09] |
頁 次 | 頁462-467+CA86 |
分類號 | 417.55 |
關鍵詞 | C3值; 生長激素; 甲基丙二酸血症; 體重; C3; Growth hormone; Methylmalonic acidemia; Weight; |
語 文 | 英文(English) |
英文摘要 | Background: Information regarding growth hormone (GH) therapy in neonatal patients with methylmalonic acidemia (MMA) is lacking. We present our experience with GH therapy in neonatal patients with MMA. Methods: Four neonatal patients with mut0 type MMA were identified through newborn screening for elevated propionylcarnitine (C3) levels. GH therapy (0.6 IU/kg/week, subcutaneously) was prescribed for patient 1 after 1 month of admission, and was prescribed for patients 2, 3 and 4 on the 1st day of admission. We evaluated weight, skin erosion, hospital stay, and serum levels of C3 after GH therapy. Results: All of the neonatal patients with MMA displayed obvious weight gain and distinct improvement in skin erosions after GH therapy. The duration of hospital stay for patients 2, 3 and 4 was reduced compared to that of patient 1. However, the metabolic effects of GH therapy on reducing serum levels of C3 seem to be indeterminate. Conclusion: Our clinical findings suggest that GH therapy has potentially beneficial effects on neonatal patients with MMA. |
本系統中英文摘要資訊取自各篇刊載內容。