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題 名 | Long-Term Follow-Up of Congenital Aniridia--A Case Report=先天性無虹膜症之長期追蹤--病例報告 |
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作 者 | 郭昱宏; 林安斐; 劉郁琦; 李淑美; | 書刊名 | 中華民國眼科醫學會雜誌 |
卷 期 | 49:2 2010.06[民99.06] |
頁 次 | 頁192-196 |
分類號 | 416.744 |
關鍵詞 | 白內障; 先天性無虹膜症; 人工水晶體; Congenital aniridia; Suture-intraocular lens implantation; |
語 文 | 英文(English) |
中文摘要 | 目的:報告一位先天性無虹膜症之病患接受手術治療後之臨床病程及結果。方法:病例報告。結果:一位27歲男性患有雙眼先天性白內障並在23年前接受過右眼白內障手術。從小雙眼視力模糊並且畏光於是來門診就診。門診右眼最佳矯正視力為零點三,右眼眼壓為26毫米汞柱。此外也有眼球震顫情形。裂隙燈下檢查發現右眼無品體合併纖維化後囊,局部周邊虹膜前沾黏,玻璃體前突出;雙眼無虹膜。散瞳眼底檢查可見雙眼中心凹發育不全。於是為該病人右眼進行人工水晶體縫合置入,小樑切開術,前玻璃體切除術。並且在術後一年追蹤時右眼最佳矯正視力保持在零點三且眼壓得到良好控制。結論:先天性無虹膜症很少見且常常有很多眼科台併症。目前有很多不同手術方式。我們選擇為病人進行人工水晶體縫合置入術,並巨有令人滿意的手術結果。 |
英文摘要 | Purpose: To report the clinical course and the surgical outcomes of a patient of congenital hereditary aniridia. Results: A 27-year-old male with a history of bilateral congenital aniridia and cataract had undergone cataract extraction on his right eye at the age of 4. He suffered from blurred vision and photophobia of both eyes since childhood. On examination, the best corrected visual acuity (BCVA) was 6/20 and the intraocular pressure (IOP) was 26 mmHg in the right eye. Nystagmus was noted. Slit lamp biomicroscopy showed incomplete aniridia in both eyes, aphakia with fibrotic capsular bag, focal peripheral anterior synechiae and prolapsed vitreous in the right eye. Fundus examination revealed bilateral foveal hypoplasia. We perfomed sutured-intraocular lens (IOL) implantation, trabeculectomy, and anterior vitrectomy on his right eye. The BCVA preserved at 6/20 with well-controlled IOP at one year's follow-up. Conclusion: Congenital aniridia is rare and causes a variety of ocular complications. There are various surgical managements at present. We chose sutured-IOL and trabeculectomy for this patient and got satisfactory outcomes. |
本系統中英文摘要資訊取自各篇刊載內容。