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題 名 | An Analysis of Endocrine Abnormalities in Adolescents and Adults with Craniopharyngioma=青少年及成年人的顱咽瘤之內分泌異常之分析 |
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作 者 | 張志任; 羅永欽; 關暟麗; 洪純隆; | 書刊名 | Medical Journal of South Taiwan |
卷 期 | 3:2 2007.09[民96.09] |
頁 次 | 頁69-75 |
分類號 | 416.29 |
關鍵詞 | 顱咽瘤; 內分泌; Craniopharyngioma; Sellar tumor; Endocrine; |
語 文 | 英文(English) |
中文摘要 | 顱咽瘤已知為青少年最常見的腦垂腺及下視丘腫瘤,也佔成年人蝶鞍內或鞍上腫瘤的二十個百分點。大部分的患者在就醫時,就有內分泌系統的問題。但僅有少數患者尋求醫療資源的協助。在過去十年中,有26位患有顱咽瘤,在高雄醫學大學附設醫院接受治療。其中有1位年紀少於14 歲、10位青少年及15位為成年患者。治療前內分泌檢查顯示7位青少年患者有生長激素失調或身高低於正常值下方的百分之十,5位為成年患者有生長激素低於正常值。在性腺賀爾蒙激素上,9位青少年患者有性腺賀爾蒙失調,1位為成年患者有性腺賀爾蒙低於正常值。在促甲狀腺分泌激素上,2位青少年患者有賀爾蒙失調,1位為成年患者有賀爾蒙低於正常值。在臨床徵狀上,患有顱咽瘤的青少年患者常常因為腦垂腺的不成熟及發育中的標的器官必須靠賀爾蒙來發育。所表現出來的徵狀就和成年患者有所不同。在病理上,青少年患者及成年患者兩者的結果也截然不同,青少年患者顱咽瘤的病理報告以扁平乳突細胞為主;成年患者顱咽瘤的病理報告以齒釉質細胞為主。種種的因素造成青少年患者在治療上,除了以手術切除外,賀爾蒙尤其是生長激素的補給是非常重要,在加拿大已有以生長激素注射來矯正患童身高過矮的問題。在促腎上腺分泌激素失調時所造成的電解質不平衡,或腦下垂腺功能失調時所造成的尿奔症。所以青少年患者及成年患者在手術前後、都必須加以密切觀察並及時治療,因為如果不慎往往造成患者死亡。 |
英文摘要 | Considerable endocrine dysfunction in those who have craniopharyngioma may be anticipated, because of its promixity to the critical hormone-producing cells in the hypothalamus and pituitary gland owing to immature hypophyseal gland, poorly developed target organs in adolescents and deficiency in human hormone. In the adult patients, the above factors do not exisit except in the adjoining location to hypophyseal-hypothalamic axis, and the selected hormone deficiency is found in our study. This study revealed that the endocrine levels were different in the adults and non-adults not only preoperatively but also postoperatively. In the past decade, we enrolled 10 adolescents and 15 adults with craniopharyngiomas receiving surgical interventions at Kaohsiung Medical College hospital (KMCH). Preoperative hormonal studies revealed growth hormone deficiency in 7(70%) adolescents and 7(47%) adults, deficiencies of gonadotropic hormone in 7(70%) adolescents and one(7%) adult, and TSH deficiencies in 2(18%) adolescents and one(7%) adult. Postoperative, there were 9(90%) adolescents and 2(13%) adults with growth hormone deficiency, 7(70%) adolescents and 2(13%) adults with lower gonadotropic hormone, and 2(20%) children and 2(13%) adults with lower levels of thyroidotrcpic hormone. Six months after the patients were discharged, endocrine enrollment was done at outpatient department. The clinical symptoms, pathologic findings, the change of hormone levels postoperatively or post high-dose radiotherapy and postoperative SIAH(syndrome of inadequate antidiuretic hormone) and panhypopituitarism that reflected craniopharyngiomas in adolescents and adults were also quite different. Primary amenorrhea and dysmenorrhea was found in all the 3 girls and short stature in nearly 80% of the adolescent patients. In the adult group, decreased secondary gender characteristics and dysmenorrhea was found also in 2(33%) female adults. The visual problem was encountered in both groups also. The clinical pictures of craniopharyngiomas in adolescents were quite different from those in adults not only in pathohistological findings, clinical pictures, and endocrine levels. There existed a challenge in preoperative and postoperative care due to the occurrence of pituitary hormone deficiency. |
本系統中英文摘要資訊取自各篇刊載內容。