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題 名 | Endocrinological Management Influences Rehabilitation Outcome in Patients with Craniopharyngioma=內分泌問題之處理影響顱咽瘤患者復健之預後 |
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作 者 | 陳威良; 孟乃欣; 吳貞儀; 林建仲; 羅瑞寬; | 書刊名 | 中臺灣醫學科學雜誌 |
卷 期 | 11:1 民95.03 |
頁 次 | 頁56-61 |
分類號 | 415.938 |
關鍵詞 | 顱咽瘤; 內分泌異常; 復健; Craniopharyngioma; Endocrinopathy; Rehabilitation; |
語 文 | 英文(English) |
中文摘要 | 顱咽是一種具侵犯性之顱內腫瘤,常有視覺、神經學及內分泌之異常。手術常有腫瘤復發、全腦下垂體功能低下和尿崩症等問題。病例為37歲男性,最初主訴複視及多尿,不久便被診斷患有顱咽瘤,並於轉至本院4個月前接受手術,手術後併發右內動脈梗塞。轉至本院復健科時左側偏癱伴隨認知功能障礙,功能獨立量表只有29分。檢查顯示其有廣泛內分泌異常,在腎上腺皮質素、甲狀腺素之適當補充下,復健之進步仍有限。但補充睪固酮後,出現長足之進步,功能獨立量表於出院前達到44分。這案例顯示調整內分泌異常為顱咽瘤病患復健進步之重要角色。 |
英文摘要 | Craniopharyngioma is a benign intracranial tumor but requires aggressive intervention because of its location and invasiveness. Common clinical manifestations include visual impairment, neurological deficits and endocrinopathy. The most frequent postoperative complications are tumor recurrence, panhypopituitarism and diabetes insipidus (DI). We report a 37-year-ld man with craniopharyngioma who came to our department for rehabilitation. He had polyuria and diplopia before the intrasellar tumor had been diagnosed. He had undergone an operation four months before admission to our hospital. Immediately after surgery, he had an infarction in the right internal carotid artery territory, which caused left hemiplegia and impairment of cognitive function. He had a low functional independence measurement (FIM) score (29 out of a full score of 126) when he arrive at our department. Deficiency in thyroid hormone and cortisol, as well central diabetes insipidus were noted. The patient was given thyroxin, cortisone and desmopressin, and began a rehabilitation program; however, his condition did not significantly improve. A blood sample was drawn and a low serum androgen level was noted. We therefore decided to give him testosterone supplement. FIM score improved from 36 to 44 within 10 days of taking testosterone. This case report illustrates that proper treatment of endocrine plays a key role in successfully managing patients with craniopharyngioma. |
本系統中英文摘要資訊取自各篇刊載內容。