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頁籤選單縮合
題 名 | 重症肌無力危象的加護照顧=Critical Care in Myasthenic Crisis |
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作 者 | 邱浩彰; 葉建宏; | 書刊名 | 中華民國重症醫學雜誌 |
卷 期 | 3:2 2001.04[民90.04] |
頁 次 | 頁174-183 |
分類號 | 415.9413 |
關鍵詞 | 肌無力症; 肺功能; 靜脈免疫球蛋白; 血漿分離; Myasthenia gravis; Pulmonary function; Plasmapheresis; Intravenous immunoglobulin; |
語 文 | 中文(Chinese) |
中文摘要 | 肌無力症的治療主要原則是阻斷自體免疫反應的進行在治療的過程中,大部份的病人可利用藥物得到很好的控制,有些病人異常免疫反應較強,會造成呼吸肌力的無力,有時會對生命有威脅,稱之為危象。在早期輕微的呼吸衰竭時,病人常表現坐立不安、失眠等,常可看見呼吸時輔助性肌肉的肌肉收縮,在此若能早期偵測,及時給予治療,常對病人有相當大的幫助。肌無力症急性惡化時,緊急免疫療法可以提供及時助益,其中包括血漿分離術及靜脈免疫球蛋白注射。此二者療效相近,大約都有80%左右之成功率。 |
英文摘要 | Patients with myasthenic gravis sometimes complain of difficult swallowing, chewing or speaking. The risks of aspiration of gastric contents and position-dependent airway obstruction are well known in myasthenic patients whose bulbar muscle have been weakened. Myasthenic crisis, defined as respiratory failure requiring mechanical ventilation, is a potentially life-threatening complication. Paradoxical movement of the abdomen and thoracic cage, sue of the accessory respiratory muscles and an increase in the respiratory rate herald ventilatory failure due to respiratory muscle weakness. Rapid deterioration of respiratory function may occur as a result of infection, retention of excessive secretions due to an ineffective cough or anticholinesterase overdose. Serial monitoring of pulmonary function tests may detect impending ventilaory failure. Patients with myasthenic crisis should be transferred to a critical care unit, undergo elective endoracheal intubation and begin mechanical ventilation. Anticholinesterase should be decreased/discontinued after ventilatory support is initiated to avoid precipitating cholinergic effects. Plasmapheresis has been shown to be a successful therapy for patients with MG in crisis or fulminant progression. Intravenous immunoglobulin treatment is reserved for patients with very difficult venous access, patients with possible sepsis as a trigger for crisis, and perhaps, children. Any MG patient with progressive dysphagia or dyspnea should be treated with plasmapheresis to prevent the development of crisis or related complication. |
本系統中英文摘要資訊取自各篇刊載內容。