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題 名 | Primary Vaginal Extraosseous Ewing Sarcoma/Primitive Neuroectodermal Tumor with Cranial Metastasis=陰道原發性骨骼外尤文氏肉瘤/原始神經外胚葉腫瘤轉移至頭部 |
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作 者 | 葉致文; 許書雄; 張乃仁; 王志生; 廖維專; 陳俊逸; 劉斯顥; 陳志豪; | 書刊名 | Journal of the Chinese Medical Association |
卷 期 | 72:6 2009.06[民98.06] |
頁 次 | 頁332-335+CA61 |
分類號 | 417.38 |
關鍵詞 | 骨骼外尤文氏肉瘤; 轉移; 陰道; PNET; Extraosseous Ewing sarcoma; Metastasis; Vagina; |
語 文 | 英文(English) |
英文摘要 | Extraosseous Ewing sarcoma is now regarded as a member of the Ewing sarcoma/primitive neuroectodermal tumor (PNET) family. It typically involves the soft tissues of the chest wall, pelvis, paravertebral region, abdominal wall, retroperitoneal region and extremities of children, adolescents and young adults, but it seldom occurs in the female genital tract. We report an extremely rare case of retrospective diagnosis of vaginal extraosseous Ewing sarcoma/PNET which metastasized to the right frontoparietal scalp, skull, and dura. Surgical resection, followed by adjuvant radiotherapy and chemotherapy resulted in a favourable clinical outcome. Both the vaginal and head tumors had similar light microscopic features supporting the diagnosis. |
本系統中英文摘要資訊取自各篇刊載內容。