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題 名 | Clinical Analysis of Bronchiectasis in Taiwanese Children=臺灣兒童支氣管擴張症之臨床分析 |
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作 者 | 賴申豪; 黃健燊; 廖穗綾; | 書刊名 | 長庚醫學 |
卷 期 | 27:2 2004.02[民93.02] |
頁 次 | 頁122-128 |
分類號 | 415.425 |
關鍵詞 | 兒童; 支氣管擴張症; Bronchiectasis; Children; |
語 文 | 英文(English) |
中文摘要 | 背景:在囊狀纖維化(cystic fibrosis)盛行率極低之非高加索人兒童中,支氣管擴張症之臨床表現及致病原因在過去罕為描述。此份報告旨在描述臺灣兒童支氣管擴張症之臨床特徵。 方法:經由回溯性的病歷分析,自1991年至2001年中計有29例診斷為支氣管擴張症之兒童。每一例皆由高解析度電腦斷層獲得診斷。藉由病歷記錄分析其基本資料,臨床表現,肺功能報告與微生物檢查。我們亦檢視其放射學檢查,並儘可能探究造成支氣管擴張症之原因。 結果:此次研究中計有17個女孩及12個男孩,平均年齡11.0±3.9歲。持續性之慢性咳嗽,終日之痰液生成與咳血為常見症狀。肺囉音喘鳴音為理學檢查中最常見之發現。先前之下呼吸道感染,氣喘與原發性之免疫功能缺損為常見之致病因,但仍有31.0%的病例查不出可能致病因。居下位的肺葉為常影響之位置,有89.7%的病童左下葉,右下葉亦有69.0%;而同時合併有鼻竇炎者亦佔70.6%。在接受肺功能檢查之病童中,大部分皆呈現輕度之呼吸道阻塞。從痰液或支氣管肺泡沖洗液之微生物檢查中,大部分檢體(52.2%)有發現;其中Pseudomonas aeruginosa, Hemophilus influenzae和Streptococcus pneumoniae為常見病菌。 結論:就90年代非高加索族群的北臺灣兒童而言,下呼吸道感染後的持續性發炎變化仍是支氣管擴張症的重要原因。超過三分之二的病童有其潛在之易致病因子,諸如氣喘,免疫功能缺損及吞嚥障礙。即使在此囊狀纖維化盛行率極低之地區,凡兒童有慢性化膿性之痰液生成和持續的肺囉音時,皆必須考慮支氣管擴張症的可能。 |
英文摘要 | Background: The clinical features and etiology of bronchiectasic have rarely been described in non-Caucasian populations, of whom the prevalence of cystic fibrosis is low. In this report, we studied the clinical features of bronchiectasis in Taiwanese children. Mehods: Using a retrospective chart review, 29 cases of bronchiectasis were diagnosed from 1991 through 2001. For each case, the diagnosis was confirmed using high-resolution computed tomography. Medical records were analyzed for demographic data, clinical presentation, spirometric data, and microbial isolation. Radiographic findings were reviewed, and possible causes of bronchiectasis were also identified. Results: There were 17 girls and 12 boys enrolled. Persistent cough, daily sputum production, and hemoptysis were common presenting symptoms. Crackles and wheezing were the most frequent findings during the physical examination. Previous lower airway infection, asthma, and primary immunodeficiency were the most common, but 31.0% of the cases had unknown causes. Dependent lobes were involved more frequently. Simultaneous sinusitis was noted in 70.6% of the cases. Spirometry showed mild airway obstruction in most of the cases. Most specimens (52.2%) from lower airway secretions yielded bacterial pathogens, most commonly pseudomonas aeruginosa, Haemophilus influenzae and Streptococcus pneumoniae. Conclusion: Continuing post-infectious inflammatory changes remains the most important cause of bronchiectasis in a non-Caucasian pediatric population in Northern Taiwan in the 1990s. More than two thirds of these patients had underlying predisposing factors including asthma, immunodeficiency, and swallowing dysfunction. Chronic productive purulent respiratory secretions and persistent crackles should raise the possibility of bronchiectasic in children even in Taiwan where the incidence of cystic fibrosis is low. |
本系統中英文摘要資訊取自各篇刊載內容。