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頁籤選單縮合
題 名 | Retina Pathology of a Failed External Beam-Radiated Group Vb Retinoblastoma=以放射線治療視網膜母細胞瘤之視網膜病理解剖 |
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作 者 | 譚欣媛; 陳賢立; 陳成彥; 李文浩; | 書刊名 | 長庚醫學 |
卷 期 | 25:8 2002.08[民91.08] |
頁 次 | 頁542-547 |
分類號 | 416.746 |
關鍵詞 | 視網膜母細胞瘤; 放射線治療; Retinoblastoma; External beam radiation therapy; |
語 文 | 英文(English) |
中文摘要 | 本病例為7個月大的男孩以右眼出現白色瞳孔反射作為右眼視網膜母細胞瘤之初步表現。眼部檢查發現一個大型視網膜腫瘤,並有廣泛的玻璃體癌細胞轉移,符合Reese-Ellsworth第五期之分類。初步先採用放射線治療;起初有明顯的腫瘤消退,但3個月後病情擴展成全視網膜剝離,故隨渡施與眼琅摘除術。病理解剖可見顯筐化的殘餘腫瘤,並在腫瘤周圍有纖維化及血管增生,顯示放射線治療對此第五期視網膜母細胞瘤有著不完全的療效。本視以視網膜病理解剖的角度,來佐證放射線治療對於視網膜母細胞瘤治療之重要性。 |
英文摘要 | We report on a 7-month-old boy who suffered from retinoblastoma with presentation of a white papillary reflex in his right eye. Initial examination showed a large subretinal and intraregional mass nasally with extensive vitreous seeding of tumor cells (Group Vb in the Reese-Ellsworth Classification). External beam radiation therapy (EBRT) was applied in hopes of preserving the eye, and significant regression with disappearance of vitreous seedings and a prominently decreased tumor mass with localized calcification were documented. Unfortunately total retinal detachment was subsequently identified 3 months after irradiation. The patient ultimately underwent enucleation, and histopathology revealed significant calcification within the residual tumor without marked necrosis; a preretinal fibrous membrane with focal vascular thickening was noted, which implied a partial but incomplete effect of EBRT for this group Vb retinoblastoma. We describe the histopatholgoical findings of the failure of irradiation for a group Vb retinoblastoma, and emphasize the importance of early application of EBRT treatment for a retinoblastoma. |
本系統中英文摘要資訊取自各篇刊載內容。