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題 名 | Advanced Bilateral Retinoblastoma Treated Conservatively with Lens Sparing External Beam Radiation Therapy: Report of Three Cases=重度雙側性視網膜母細胞瘤以放射線治療之結果:三例報告 |
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作 者 | 高玲玉; 曾雁明; | 書刊名 | 長庚醫學 |
卷 期 | 22:1 1999.03[民88.03] |
頁 次 | 頁100-105 |
分類號 | 416.749 |
關鍵詞 | 重度視網膜母細胞瘤; 放射線治療; Advanced retinoblastoma; External beam radiation therapy; |
語 文 | 英文(English) |
中文摘要 | 視網膜母細胞的治療,在以前的年代,眼球摘除是主要的治療方式,但病人將永 久喪失患眼的視力。重度的雙側性視網膜母細胞瘤,倘施以雙側性眼球摘除,將造成病人終 生的悲慘命運。近年來,治療的趨勢已逐漸傾向於,在不影響病人的存活率下,以較保守的 方式保存病人的患眼,並儘可能的保留患眼的視力。自 1995 年 1998 年間共有 3 例 6 隻 眼睛罹患重度雙側性視網膜母細胞瘤的病例,接受避開水晶體的放射線治療,治療的劑量自 5400 cGy 至 5700 cGy,治療次數自 27 至 28 次間,期間自 34 至 35 天不等。追�j時間 自治療結束後 14 個月至 36 個月不等。 3 位病人全數存活( 100 %),3 隻眼球在放射 線治療後腫瘤復發,1 例新生腫瘤,其中 3 眼接受眼球摘除術, 1 眼在腫瘤復發後拒作眼 球摘除術,導致視神經蔓延,其後接受化學治療,目前眼球萎縮失明,但仍然存活。眼球保 持正常外觀的比率為 2 ╱ 6 ( 33.3 %),有 1 例保持接近正常的視力 20 ╱ 30,1 例 保留有週邊視力,4 隻眼睛完全喪失視力,其中 1 例雙眼全無光覺。 重度雙側性視網膜母 細胞瘤以雙側同時作放射線治療,並不會增加病人的死亡率,且可以讓患者享受保存部分視 力的好處。 |
英文摘要 | From 1995 through 1998, 3 children with bilateral advanced retinoblastoma were treated primarily with external beam radiation therapy; 6 eyes were irradiated with a lens sparing technique, doses varied from 5500 to 5700 cGy, and follow-up period ranged from 14 to 36 months. Recurrent tumors were found in 3 eyes, and a new growing tumor in one eye. Three eyes underwent enucleation eventually; one eye refused enucleation and finally developed optic nerve extension. The overall ocular cure rate was 2/6 (33.3%). One eye sustained visual acuity of 20/30, the other eye retained some peripheral vision; both eyes were blind in one patient. There were no deaths, metastasis, or secondary malignant tumors in our study. Advanced bilateral retinoblastoma with simultaneous radiation therapy instead of bilateral enucleation does not increase the risk of death, and more children will enjoy the benefits of retaining some vision in the affected eye through the use of this conservative therapeutic regimen. |
本系統中英文摘要資訊取自各篇刊載內容。