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題 名 | Monini氏內耳發育不全併發反覆性腦膜炎--二例報告=Mondini Dysplasia with Recurrent Meningitis--Report of Two Cases |
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作 者 | 施水木; 徐銘燦; 林鴻清; 張克昌; 黃榮貴; | 書刊名 | 中華民國耳鼻喉科醫學雜誌 |
卷 期 | 34:2 民88.03-04 |
頁 次 | 頁165-168 |
分類號 | 416.81 |
關鍵詞 | Mondini氏內耳發育不全; 腦膜炎; Mondini dysplasia; Meningitis; |
語 文 | 中文(Chinese) |
中文摘要 | Mondini 氏內耳發育不全是一種包括骨性及膜性迷路的發育不全,可能是單側或 雙側。患者常有重度聽力障礙及前庭功能低下,且常合併骨性迷路內壁及外壁�硎煄A使腦脊 髓液或外淋巴液與中耳腔交通, 造成腦脊髓液鼻漏及反覆性腦膜炎的表現。 本院於 1994 年 12 月及 1996 年 12 月分別經歷 1 例耳源性反覆性腦膜炎的病例,經電腦斷層掃描檢 查診斷為 Mondini 氏內耳發育不全,其中第 1 例是兩側性異常。並經鼓室探查術證實有外 淋巴液自卵圓窗溢出,第 2 例於手術時有外淋巴液大量湧出的現象。 之後分別以顳肌膜、 顳肌及碎骨片經卵圓窗將前庭充填,以阻止腦脊髓液外漏。術後情況良好,在門診追蹤玉今 並無腦膜炎復發情形。 |
英文摘要 | Mondini dysplasia is a congenital inner ear malformation chaacterized by incomplete formation of the bony and membranous labyrinths. Affected patients usually present with profound sensorineural hearing loss, peripheral vestibular hypofunction, and recurrent meningitis. We report two cases of otogenic recurrent meningitis. Computed tomography showed bilateral Mondini dysplasia in case 1 and right Mondini dysplasia in case 2. Exploratory tympanotomy revealed perilymph leakage from the oval windows in both cases. Stapedectomy and vestibular obliteration with fascia, muscle, and bone were performed. Meningitis has not occurred postoperatively after 44 and 20 months of follow-up in these two patients. |
本系統中英文摘要資訊取自各篇刊載內容。