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頁籤選單縮合
題 名 | Bacterial Meningitis of an Infant with Currarino Triad=Currarino三表徵的嬰兒併發細菌性腦膜炎:一病例報告 |
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作 者 | 周宜卿; 麥淑珍; 林大丕; 遲景上; 彭海祁; | 書刊名 | 臺灣兒科醫學會雜誌 |
卷 期 | 43:5 民91.09-10 |
頁 次 | 頁288-290+306 |
分類號 | 417.5157 |
關鍵詞 | Currarino三表徵; 肛門直腸畸型; 薦骨缺損; 薦骨前質塊; 腦膜炎; Currarino triad; Anorectal malformation; Sacral anomaly; Presacral mass; Meningitis; |
語 文 | 英文(English) |
中文摘要 | Currarino三表徵是一罕見遺傳性疾病,包括肛門直腸畸型,薦骨缺損,與薦骨前質塊。大多數報告爲顯性遺傳。我們報告一句三個月大的Currarino triad病例,因細菌性腦膜炎併發急性蜘蛛網膜發炎,而導致下肢癱瘓。因爲遺傳性疾病,故檢查其他兄弟姐妹,發現其兄弟爲一不完全型。提出此病例的目的,在於強調早期診斷的重要性,以期早期切除質塊,避免後遺症,並應作遺傳諮詢。 |
英文摘要 | Currarino triad is a rarely hereditary condition including: (1) an anorectal malformation, (2) an anterior sacral defect, and (3) a presacral mass. Autosomal dominant transmission is suggested. We reported one case of Currarino triad, who was a 3-month-old male with sacral dysgenesis, imperforated anus and enteric cyst. This case presented with acute lower limbs paralysis due to bacterial meningitis complicated with acute arachnoiditis. The diagnosis of this condition led to a work-up of his sibling, who was found to have an incomplete type. The purpose of this case is to emphasize that a high index of suspicion for timely diagnosis and treatment of Currarino triad could prevent devastating complications. |
本系統中英文摘要資訊取自各篇刊載內容。