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題 名 | Familial Mediterranean Fever in a Taiwanese Patient=地中海熱一臺灣病例報告 |
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作 者 | 蔡文展; 顏正賢; 陳忠仁; 蔡季君; 歐燦騰; 劉宏文; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 17:4 2001.04[民90.04] |
頁 次 | 頁212-215 |
分類號 | 415.2 |
關鍵詞 | 地中海熱; 臺灣; Familial mediterranean fever; Colchicine; Recurrent polyser-ositis; |
語 文 | 英文(English) |
中文摘要 | 地中海熱 (Familial Mediterranean Fever)是一種罕見的家族性疾病; 主 要是以週期性的發燒, 漿膜炎來表現. 本篇報告發表一位22歲的男性,十餘年來 每隔二三週即發生週期性的發燒, 漿膜炎; 雖然他遍訪數家醫院, 並且在十五歲 時被診斷為闌尾炎, 並接受開刀治療, 還是沒有得到正確的診斷與治療. 此次住 院當中, 除了稍微的白血球與C-反應蛋白偏高以外, 很多實驗室檢查皆正常. 影 像學檢查包括胸部x光, 腹部電腦斷層均正常. 但有趣的是Gallium-67掃描發現 在右胸及右下腹出現強烈反應. 經診斷為地中海熱後給予秋水仙素預防性治療. 病人已經超過二年沒有復發。 |
英文摘要 | Familial Mediterranean fever is a rare disease characterized by cyclic attacks of fever, serositis and strong family background. Here we report a 22-year-old man who suffered from recurrent fever accompanied by chest and abdominal pain for more than 10 years. The attack frequency was about once per 2-3 weeks. Although he consulted many clinics and even received appendectomy at the age of 15, no definite diagnosis was given. During the admission, many laboratory examinations failed to show any abnormality except mild leukocytosis and elevated C-reaction protein. Image studies including chest X ray and abdominal CT scan showed negative result but, interestingly, Gallium-67 scan showed a hot spot in right lower chest and right lower abdomen. After prophylaxis with colchicine 1.0 mg per day, he has enjoyed more than 2 years without the above symptoms. |
本系統中英文摘要資訊取自各篇刊載內容。