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題 名 | Food Protein-induced Enterocolitis Syndrome: Report of One Case=食物蛋白誘發腸炎症候群:一病例報告 |
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作 者 | 馬漢儼; 陳五常; 林隆煌; | 書刊名 | 臺灣兒科醫學會雜誌 |
卷 期 | 42:1 民90.01-02 |
頁 次 | 頁49-52 |
分類號 | 417.517 |
關鍵詞 | 食物蛋白; 腸炎症候群; 嬰兒; Food protein-induced enterocolitis syndrome; FPIES; Double-blind placebo-controlled food challenge; DBPCFC; |
語 文 | 英文(English) |
中文摘要 | 本文報告一位76天大的男嬰,他在2週大時罹患腹瀉,一開始被診斷爲急性腸胃炎,産以一般嬰兒奶粉噮食。因爲病人出現持續性腹瀉,先以豆蛋白配方奶粉餵食再改高度水解蛋白本方奶粉餵食,腹瀉情形明顯獲得改善。但數天後,當家屬自行將高度水解性配方奶粉換回一般嬰兒配方奶粉後,病人又出現了嚴重的腹瀉並伴隨著務絲便、嘔吐、脫水等症狀。根據臨床症狀及病史,牛奶過敏是最初的憶斷。先以全靜脈營養5天,然後開始以高度水解蛋白配方奶粉餵食。過敏探查並未發現嗜伊紅性白血球,血清IgE正常,牛奶蛋白的特異性IgE抗體呈陰性,牛奶的即時性皮膚試驗也呈陰性。住院10天之後安排的雙盲牛奶誘發試驗引起嘔吐,腹瀉,發燒,代謝性酸中毒,重度脫水及血中中性球增加達27460/mm^3。由病人過敏檢查及誘發試驗結果分析,此病人符合“食物蛋白誘發腸炎症候群”的診斷。 |
英文摘要 | We report a 76-day old infant who got diarrhea within the first week of life. He was treated as acute gastroenterocolitis and kept on feeding with regular infant formula. Because the symptoms persisted, the feeding formula was shifted to soy-based formula then to the highly-hydrolyzed formula and got improvement. But severe bloody diarrhea, vomiting, dehydration and fever developed after feeding with regular infant formula again. Based on the history and clinical presentations, cow's milk allergy was suspected. He received total parenteral nutrition for 5 days then fed with highly-hydrolyzed formula with slowly increasing amount. Thereafter tests for total eosinophil counts, total serum IgE, milk specific IgE antibodies and milk extract skin prick test were all unremarkable. Under the impression of food protein-induced enterocolitis syndrome (FPIES), a double-blind placebo-controlled food challenge (DBPCFC) with infant formula was performed. Regular infant formula induced severe vomiting, diarrhea, fever, acidosis and elevation of absolute neutrophil counts (ANC) of peripheral blood by 27640/mm3. Based on the laboratory findings and challenge results, the patient fit the diagnostic criteria of food protein-induced enterocolitis syndrome. |
本系統中英文摘要資訊取自各篇刊載內容。