查詢結果分析
相關文獻
- Hirayama Disease: A Report of Two Cases
- 硬脊膜外麻醉導致下半身癱瘓:病例報告
- Gadolinium-Enhanced MRI in Neuro-Behcet Disease
- Magnetic Resonance Images of Neuronal Migration Anomalies
- 擴散影像在腦缺血及梗塞診斷上的應用價值
- Lumbar Synovial Cysts: Magnetic Resonance Imaging Evaluation
- Orbital Invasion in Nasopharyngeal Carcinoma: Evaluation with Computed Tomography and Magnetic Resonance Imaging
- Primary Cardiac Tumors: Report of Two Cases
- Magnetic Resonance Imaging Features of Neuro-Behcet's Disease: A Case Report
- A Rotational Phantom for Evaluation of MR-Compatible Biopsy Devices: Experiment and Preliminary Observations
頁籤選單縮合
題 名 | Hirayama Disease: A Report of Two Cases |
---|---|
作 者 | Tseng, Chun-hung; Wang, Pao-yu; | 書刊名 | Acta Neurologica Taiwanica |
卷 期 | 9:4 民89.12 |
頁 次 | 頁297-302 |
分類號 | 415.9413 |
關鍵詞 | 運動神經元疾病; 磁振造影; Hirayama disease; Motor neuron disease; Magnetic resonance image; |
語 文 | 英文(English) |
英文摘要 | We present two young men with progressive weakness, occasional fasciculation, and wasting of their thenar, hypothenar and forearm flexor muscles. Neither evidence of involvement of the upper motor neurons, nor sensory impairment was found. Hirayama disease, a rare form of focal segmental motor neuron disease of lower cervical spinal cord, especially at C7, C8 and T1, was diagnosed after assessing results of clinical and electrophysiological studies. Hirayama disease is usually noted in young Asian males between the ages of 15 and 25 years, and was usually asymmetric with involvement of unilateral upper limbs. On magnetic resonance images of the cervical spine, neither of our two patients showed abnormalities over the cervical spine and spinal cord on the nature posture, or abnormal vascular engorgement behind the cervical spinal cord on the neck flexion. |
本系統中英文摘要資訊取自各篇刊載內容。