頁籤選單縮合
題 名 | Solitary Fibrous Tumor in the Pelvis--A Case Report and Review of the Literature=骨盆腔之孤立纖維腫瘤:一病例報告及文獻回顧 |
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作 者 | 林憲雄; 楊文宏; 唐一清; 戴元昌; | 書刊名 | 中華民國泌尿科醫學會雜誌 |
卷 期 | 10:4 1999.12[民88.12] |
頁 次 | 頁168-172 |
分類號 | 415.8 |
關鍵詞 | 孤立纖維腫瘤; 梭狀細胞腫瘤; Solitary fibrous tumor; Spindle cell neoplasm; |
語 文 | 英文(English) |
中文摘要 | 孤立纖維腫瘤是一相當罕見的梭狀細胞腫瘤,它通常長在助膜的地方,但近年來,在身體其他部位陸陸續續有人發表出來,因此長在助膜外的孤立纖維腫瘤往往被誤診或未能辨識。我們報導一例59歲男性患者,入院主訴為急性尿液瀦流。影像學檢查發現介於膀胱和直腸之間有一直徑約10公分的異質性軟組織腫瘤。經直腸超音波切片病理診斷為惡性梭狀細胞腫瘤。病患接受腫瘤完全切除手術。微觀下,此病變是一界線明確的腫瘤,它由無規則的梭狀細胞雜亂的排列而成,中間夾雜著大小不一的膠原纖維。另外,亦可見豐富的上管及呈現血管外皮細胞瘤的型態。在免疫組織學上,腫瘤細胞對desmin和S-100呈現陰性反應,對CD34和bcl2呈現瀰漫的陽性反應。最終的臨床病理診斷為孤立纖維腫瘤。此病患到目前為止仍定期於門診追蹤,健康情形良好。總結來說,孤立纖維腫瘤應晚入骨盆腫瘤的鑑別診斷中。文中並作文獻回顧。 |
英文摘要 | Solitary fibrous tumors (SFTs) are rare spindle cell neoplasms that were originally de-scribed in the pleura but can occur in a variety of sites, as a consequence of which extrapleural examples often go unrecongnized or misdiagnosed. We report an SFT arising in the pelvis in a 59-year-old male with presentation of acute urinary retention. Image studies showed a huge (10 cm in maximum diameter) hetrogenous soft tissue tumor between the urinary bladder and rectum. Transrectal sonoguided biopsy suggested malignant spindle-cell tumor or leiomyosarcoma. The tumor was excised completely. Microscopically, the lesion was well circumscribed, and com-posed of pattern-less spindle cells without mitoses, in a variably collagenous background. Abun-dant vasculature and focal hemangiopericytoma-like pattern were noted. Immunohistochemically, the tumor cells were negative for desmin and S-100 but diffusely positive for CD 34 and bc1-2. The overall features suggest a solitary fibrous tumor. So far, the patient is regularly followed at our out-patient clinic with a benign clinical course. In conclusion, SFT should e included in the differential diagnosis of tumors arising in the pelvis. The literature is also reviewed. |
本系統中英文摘要資訊取自各篇刊載內容。