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題 名 | Dohi氏網狀肢端色素沉著症--病例報告及文獻回顧=Reticulate Acropigmentation of Dohi--A Case Report and Review of Literature |
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作 者 | 趙昭明; 汪經堯; 瞿德璐; | 書刊名 | 國防醫學 |
卷 期 | 29:1 1999.07[民88.07] |
頁 次 | 頁73-76 |
分類號 | 415.687 |
關鍵詞 | 網狀; 肢端色素沈著; Reticulate; Acropigmentation; Dohi; |
語 文 | 中文(Chinese) |
中文摘要 | 網狀肢端色素沈著為一種皮膚變色疾病的族群,臨床上通常是一種自體顯性遺傳 的模式表現。 Kitamura 氏與 Dohi 氏為兩種主要的網狀肢端色素沈著病,其中 DOhi 氏網 狀肢端色素沈著的特徵是四肢的皮膚呈現以網狀形式排列的色素斑和去色素斑。我們報告一 例 20 歲的男性其前臂內側及手背皮膚有漸進性的網狀色素變深, 他的父親與他有相似的皮 膚病灶。皮膚組織病理檢查顯示在基底層區有交互色素沈著及變淡的變化,與臨床診斷相符 合。 |
英文摘要 | Reticulate acropigmentation ( RA ) comprises dyschromic disorders that generally have an autosomal dominant pattern of inheritance. Reticulate acropigmentation of Dohi (RAD) is characterized by pigmented and depigmented macules mixed in a reticulate pattern on the extremities. We reported a 20-year-old man who had progressive reticulate hypo-pigmented macules on the volar surface of his forearms and the dorsa of his hands. His father also has similar lesions. Histopathologic examination revealed alternative hyperpigmentation and hypopigmentation in basal layer of epidermis. |
本系統中英文摘要資訊取自各篇刊載內容。