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題 名 | Clinical Manifestations and Treatment of Marfan Syndrome: A Case Report=Marfan症候群的症狀表現及治療:一病例報告 |
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作 者 | 林永崇; 郭三元; 賴振宏; 張木蘭; 朱士傑; 張德明; | 書刊名 | 醫學研究 |
卷 期 | 19:6 1999.05[民88.05] |
頁 次 | 頁360-364 |
分類號 | 415.3 |
關鍵詞 | Marfan症候群; 蛛狀指; 主動脈瘤; Marfan syndrome; Arachnodactyly; Aortic aneurysm; |
語 文 | 英文(English) |
中文摘要 | Marfan症候群是以骨骼系統異常,及眼球晶體異位及主動脈徑擴大所組成的症候群。我們報告一位20歲男性患者呈現出蛛狀手指、脊柱彎曲及雞胸、心藏超音波呈現主動脈擴大,二尖瓣脫垂。由臨床症狀、心藏超音波及放射學檢查,診斷出Marfan症候群。由於心藏血管的異常是造成主要病患症狀及死亡。目前尚無確切的治療方法。但數個研究結果均建議貝他交感神經阻斷劑有助於延緩或預防主動脈擴大。 |
英文摘要 | Marfan syndrome is characterized by a triad of features with long, thin extremities associated with other skeletal changes, ectopia lentis, and aortic aneurysm. A 20-year-old male presented with arachnodactyly, scoliosis and chest wall deformity. Echocardiogram showed the aortic root dilatation, mirtral valve prolapse. The diagnosis of Marfan syndrome was based on the clinical manifestation. It was demonstrated by clinical picture, chocardiorgram and roentgenologic test. The cardiovascular abnormalities are the major source of morbidity and mortality. There is no established treatment, but several investigations had recommended use of beta-adrenergic blocker to delay or prevent aortic dilatation. |
本系統中英文摘要資訊取自各篇刊載內容。