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題 名 | The Need for Changes in Diagnostic Criteria for Kawasaki Disease in Infants=嬰兒罹患川崎病其診斷標準有修改的必要 |
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作 者 | 邢學平; 黃碧桃; 傅雲慶; 陸振翮; 孟春昌; | 書刊名 | Acta Cardiologica Sinica |
卷 期 | 15:1 1999.01[民88.01] |
頁 次 | 頁17-24 |
分類號 | 417.5222 |
關鍵詞 | 川崎病; 血尹炎; 冠狀動脈瘤; Kawasaki disease; Vascultis; Coronary artery aneurysm; |
語 文 | 英文(English) |
中文摘要 | 背景:嬰兒罹患川崎病通常有非典型的臨床表現及較高的併發症, 導致延遲診斷及治療。 方法:根據本院從1988到1996年所有81個川崎病童病歷記錄加以分析,其中有20個(25%)是嬰兒,另外有61個(75%)是大於一歲的孩童。在81個病人中,有21個(25%)顯示非典型的川崎病臨床表現,其中又以嬰兒占較高的比例(45%比19%;P=0.02)。 結果:冠狀動脈病變較在嬰兒(45%)較一歲以上之孩童(19%)為多(P < 0.05)。頸部淋巴結的診斷在嬰兒身上幾乎看不見。川崎病的嬰兒中早期接受免疫球蛋白治療者,則不會產生冠狀動脈病變。 結論:根據本研究結果,我們發現目前診斷標準應用於嬰兒可能無法達到早期診斷的價值。因此,建議部份修改現行的川崎病診斷標準以適用於嬰兒的年齡層。 |
英文摘要 | Background: Infants with Kawasaki disease commonly have atypical presentations and a higher complication rate, likely related to delayed diagnosis and treatment. Methods: A total of 81 cases with Kawasake disease who were treated at our hospital from 1988 to 1996 were analyzed retrospectively. Among them, 21 (25%) had atypical presentations of Kawasaki disease. Of the 21 patients who presented with atypical presentation of Kawasaki disease, 9 (45%) were infants and 12 were children older than one year. Results: Infants had a higher incidence of atypical Kawasaki disease [9 (45%) versus 12 (19%); P=0.02] and also a higher incidence of coronary artery complications than the patients older than one year did [9(45%) versus 11 (18%); P<0.05]. Cervical lymphadenopathy was less common in infants younger than 1 year [0 (0%) versus 40 (65%)]. Other manifestations and laboratory changes were not different despite patient age. Coronary artery complications did not develop in any infants who received early intravenous immunoglobulin (IVIG) therapy. Conclusion: From this study, we found that the diagnostic criteria for Kawasaki disease are too restrictive to allow early diagnosis for infants with atypical presentation. It is suggested that the diagnostic criteria for infants with Kawasaki disease may be revised for early diagnosis. |
本系統中英文摘要資訊取自各篇刊載內容。