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題 名 | 進行性指掌角化症表皮最終分化及角質層功能異常之探討=Abnormal Expression of Epidermal Terminal Differentiation and Functional Abnormalities of the Stratum Corneum in Patients with Keratoderma Tylodes Palmaris Progressiva |
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作 者 | 陳英璋; 謝孟穎; 蔡志仁; 蔡瑞真; 許漢銘; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 17:1 1999.03[民88.03] |
頁 次 | 頁1-15 |
分類號 | 415.71 |
關鍵詞 | 進行性指掌角化症; 表皮最終分化; 角質層; 主婦濕疹; Housewives dermatitis; Epidermal differentiation; Stratum corneum; Water content; |
語 文 | 中文(Chinese) |
英文摘要 | 進行性指掌角化症(keratoderma tylodes palmaris progressiva ,KTPP;或稱 乾燥型掌部濕疹或主婦濕疹)是一種手部的慢性刺激性皮膚炎,導因於刺激原如肥皂、清潔 劑等對角質層的破壞。最近的研究顯示上述刺激原不僅會破壞角質層,同時亦導致表皮分化之 異常;然而有關KTPP之分化及角質層之變化目前所知有限。本研究著重於探討KTPP患者病變 部位角質層之功能及表皮最終分化之變化,以期對KTPP之病態生理有進一步之瞭解。結果顯 示:以表皮最終分化指標,抗profilaggrin/filaggrin抗體之免疫螢光染色檢查法,及抗 involucrin抗體之免疫過氧化氫酵素法檢查,顯示病變處之正常分化呈現散在性缺損。而另 一表皮最終分化指標,角質細胞間之中性脂肪在oil red O染色下呈現破壞之現象;進一步 以RuO�痔T定,在電子顯微鏡下觀察,可見角質細胞間脂肪膜狀結構及胞橋小體(desmosome )之變化。以上結果顯示病變部位表皮滲透障壁功能的破壞;然而測定患部之經皮水分散失 反而下降,經進一步分析,發現其發汗功能顯著降低,同時其含水量及保水機能亦顯著下降 。由以上之結果顯示,KTPP表皮之最終分化及角質層之形態及功能皆呈現異常之現象。 ed water contend and abnormal sorption-desorption test of the SC were found. Howeverm transepidermal water loss was decreased in the lesional skin, which was probably due to hypohidrosis after hand dermatitis. Our results indicate that both differentiational defects and impaired physiological function of the SC occur in KTPP. |
本系統中英文摘要資訊取自各篇刊載內容。