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題 名 | Guillain-Barre'症候群的治療原則=Current Concepts about Treatment of Guillain-Barre' Syndrome |
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作 者 | 蔡清標; | 書刊名 | 中華民國重症醫學雜誌 |
卷 期 | 3:2 2001.04[民90.04] |
頁 次 | 頁184-191 |
分類號 | 415.827 |
關鍵詞 | Guillain-Barre'症候群; 血漿置換術; 免疫球蛋白; Guillain-Barre' syndrome; Plasmapheresis; Immunoglobulin; |
語 文 | 中文(Chinese) |
中文摘要 | Guillain-Barre’ Syndrome (GBS症候群)大部分發生在40歲以前,每年平均發生率約為十萬分之1.3-1.9。這是一種自體免疫疾病,起因於身體產生的自體抗體侵犯髓鞘組織造成去髓鞘神經炎,雖然這種疾病的預後非常的良好,經過良好的照顧多半會痊癒,然而在疾病過程中約有20-30%的病患會產生呼吸肌肉麻痺,而出現呼吸衰竭的現象,另有部分患者的自主神經受到侵犯,產生心律不整、血壓降低等狀況,一般而言GBS症候群在發病後四周之內會達到高峰然後逐漸緩解,整體而言死亡率約在5%左右,目前由於呼吸治療的進步,死亡率已有逐漸下降的趨勢,早期增有常箸建議使用類固醇治療,但是效果並不明顯,且增加併發症的發生率,現已不再使用,目前的標準療法以血漿置換術及注射免疫球蛋白為主,脊髓液透析、免疫抑制劑及干擾素治療則尚在研究之中。 |
英文摘要 | Guillain-Barre’s syndrome is an acute autoimmune polyradiculoneuropathy with a clinical presentation of flaccid paralysis and areflexia, antecedent infection particularly Campylobacter jejuni gastroenteritis and the role of anti ganglioside antibody may related to the pathogenesis. Guillain-Barre syndrome occurs at the rate of 1.3-1.9 cases per 100,000 population per year, paralysis is frequently extreme, 20-30% patients requiring assisted respiration and about 5% or fewer will die of the illness, autonomic nerve system involvement like arrhythmia, hypotension sometimes exaggerated mortality, treatment with steroid is not suggested due to its side effect, plamaphersis and immunoglobulin infusion is the treatment of choice at the present time, CSF filtration or treatment with interferon are under clinical trial. |
本系統中英文摘要資訊取自各篇刊載內容。