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題 名 | Clinical Aspects of Thromboembolic Complications in Children with Nephrotic Syndrome=腎病症候群病童合併血管栓塞併發症的臨床觀察 |
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作 者 | 魏長菁; 林清淵; | 書刊名 | 臺灣腎臟醫學會雜誌 |
卷 期 | 15:3 2001.09[民90.09] |
頁 次 | 頁97-100+128 |
分類號 | 415.74 |
關鍵詞 | 血管栓塞; 腎病症候群; 預後; Thromboembolic complications; Nephrotic syndrome; Prophylaxis; Outcome; |
語 文 | 英文(English) |
中文摘要 | 血栓是腎病症候群患者中常見的併發症,如果未為能及時診斷和積極治療可能會造成致命的危險。自1991年至2001年間,腎病症候群的病童於復發期在本院接受治療時,共有八位發生血管栓塞。其中有七位病童是類固醇抗性、一位是頻繁復發型腎病症候群。六位病童在使用利尿劑和類固醇期間發生。所有的病童都有血小板增多的現象。而其他的實驗室檢查,如血紅素、血比容、膽固醇、尿蛋白、肌酸酐清除率和血栓的發生並無顯著的相關性。血栓發生的部位,以腦血管居多。大部分腦部血栓的病人有噁心、頭痛、高血壓的先兆,之後伴隨著意識突然間喪失以及抽痙。其中有二位病童有腦萎縮的後遺症。 |
英文摘要 | Thromboembolic complications (TEC), relatively frequent but serious features in children with neph-rotic syndrome (NS), require early diagnosis and intensive care. In an attempt to find the correlations between clinical aspects and the occurrence of TEC, we retrospectively studied eight children with TEC in the course of NS during a ten-year period. Seven patients were steroid resistant NS (SRNS) and one patient was frequently relapsing NS (FRNS). In laboratory tests of the coagulation system, most of the children had thrombocytosis and elevated fibrinogen. Our data also included some laboratory parameters, namel, hemoglobin, hematocrit, prothrombin time, excretory urine protein, CCr and serum cholesterol all with little predictive significance for TEC. The major iatrogenic risk factor was diuretics concomitant with corticosteroid, administered to 6 of the 8 children with TEC. The most commonly affected vessels were cerebral vesels (6 patients). Most of the patients with cerebral TEC had the prodromes of nausea, vomiting, headache and elevated systolic blood pressure, followed by the neurologic symptoms of sudden loss of consciousnessand seizure. Rare locations of TEC were also observed in mesenteric artery and deep leg veins. Prophylactic oral anticoagulation (vitamin K antagonist) was addiministrated during the new relapse until remission was achieved. No new TEC occurred under oral anticoagulation. Total resolution of thromboembolic disease was obtained in 6 patients and 2 patients had long-term sequelae of severe brain atrophy after repeated TEC. |
本系統中英文摘要資訊取自各篇刊載內容。