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題 名 | Fibrolamellar Hepatocellular Carcinoma: Report of Two Cases=纖維板層肝細胞癌:兩病例報告 |
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作 者 | 林裕民; 楊國卿; 周燕輝; 許萬盛; 陳東榮; | 書刊名 | 中華民國消化系醫學雜誌 |
卷 期 | 15:3 1998.09[民87.09] |
頁 次 | 頁8-15 |
分類號 | 416.246 |
關鍵詞 | 纖維板層肝細胞癌; Fibrolamellar Hepatocellular carcinoma; |
語 文 | 英文(English) |
中文摘要 | 肝纖維板層肝細胞癌是一種罕見的惡性腫瘤,多見於西方國家之報告,其預後比 肝細胞癌略佳。此癌症多發生於年輕成人,臨床上多數病患並無慢性肝炎或肝硬化之病史, 理學及實驗室檢查並不具特異性,影像檢查可提供部分資訊,但確立診斷仍須倚賴組織病理 檢驗。在此我們報告二個肝纖維板層癌病例:一例為典型病例;另一例則年齡偏高,且呈非 典型之核磁共振影像。此二病例均經手術治療,術後情況良好,存活至今並無腫瘤復發現象 。我們建議:在臺灣這樣肝癌好發之區域,亦應將肝纖維板層肝細胞癌列入考慮,並積極治 療,以期有較佳之預後。 |
英文摘要 | Fibrolamellar hepatocellular carcinoma is a rare malignancy seen in young adults without underlying chronic liver disease. Physical and laboratory examinations are nonspecific. Diagnosis is suspected by clinical history, supported by imaging studies and confirmed by histology. Herein we reported two cases of fibrolamellar hepatocellularcarcinoma. Patient 1 was a 30-year-old female presenting with abdominal fullness and intermittent epigastric pain for few monthes. The abdominal computed tomography showed a huge hepatic tumor with central stellate scar sormation. The hepatic angiography revealed a hypervascular mass with feeding arteries in the left hepatic lobe. These image studies favored the diagonosis of fibrolamellar hepatocellular carcinoma. Patient 2 was a 62-year-old male suffering from vague abdominal distress for few months. His computed tomography and angiography have similar findings in those of patient 1. However, the magnetic resonance revealed a markedly bright-up central scar on T2 weighted images which were atypical for fibrolamellar hepatocellular carcinoma. The laboratory values were noncontributory in these two patients. Both of them underwent expolorative laparotomy, and the tumors were successfully resected. Histopathologic features comfirmed the diagnosis of fibrolamellar hepatocellular carcinoma. These two patients were alive and well without tumor recurrence at the time of writing. We recommend that fibrolamellar hepatocellular carcinoma should be included in the differential diagnosis of hepatic tamov in Taiwan where the incidence of hepatocellular carcinoma is high and should be treated more aggressively due to its better prognosis. |
本系統中英文摘要資訊取自各篇刊載內容。