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題 名 | 近腎絲球細胞瘤導致續發性高血壓:病例報告=Secondary hypertension due to Juxtaglomerular Cell Tumor: A Case Report |
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作 者 | 陳昱宏; 葉忠信; 呂清元; 謝適仲; | 書刊名 | 中華民國家庭醫學雜誌 |
卷 期 | 8:3 1998.09[民87.09] |
頁 次 | 頁155-162 |
分類號 | 415.818 |
關鍵詞 | 近腎絲球細胞瘤; 續發性高血壓; Juxtaglomerularcell tumor; Secondary hypertension; Renin; Hyperaldosteronism; |
語 文 | 中文(Chinese) |
中文摘要 | 臨床上與頭頸部腫瘤相關之昏厥(Syncope)極為少見,它主要因腫塊壓迫頸動脈竇(Carotid sinus)或者腫瘤侵犯舌咽神經(Glossopharyngeal nerve)所造成。本文介紹壹例與頸部腫塊相關之昏厥病例,其電腦斷層攝影顯示一中心壞死性腫塊,位於右側舌基底部、口底、口咽區外側及下頷下腔區,並鄰近頸動脈分叉處。住院期間發生暫時性昏厥、合併低血壓及心跳減緩。初步診斷為血管迷走性反應(Vasovagal reflex),同時安排放射治療,但出院兩週後死亡。 痕G並無腎動脈狹窄,但右側腎靜脈血腎素濃度與左側比率大於1.5。綜合上述檢查結果,術前臨床診斷為右側腎素分泌瘤。病人經右側部份腎臟切除後,血壓即恢復正常。病理報告顯示為近腎絲球細胞瘤。此腫瘤之確認診斷需藉由光學,電子顯微鏡及免疫組織生學。臨床上當我們遇到高血壓病人合併有低血鉀,高腎素,和高醛類脂醇時,應將此病謹記在心並納入續發性高血壓之鑑別診斷中。 |
英文摘要 | Syncope is uncommon in patient with head and neck tumors, that may be produced by local compression to carotid sinue or tumor invasion to glossopharyngeal nerve. We present on case about syncope associated with neck mass. The CT scan revealed a huge central necrotic mass extending into submandibular space, oropharynx, floor of mouth and near bifurcation of carotic artery region. The syncope with hypotension, bradycardia occurred in this hopitalization course. A tentative diagnosis of vasovagal reflex was made and rediotherapy course. A tentative diagnosis of vasovagal reflex was made and rediotherapy was arranged for him. But he was died two weeks later after discharge. osis was made by a directed renal vein renin ratio blood sampling, and lateralization to the affected kidney. Light, electron microscopy and immunohistochemistry of the resected tumor confirmed the diagnosis of JGCT. Accordingly, in any hypertensive patient with hypokalemia, hyperaldosteronism and elevation of plasma renin activity, JGCT should be considered as a differential diagnosis. |
本系統中英文摘要資訊取自各篇刊載內容。