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題 名 | Sudden Cardiac Death Following Verapamil in a Patient with Wolff-Parkinson-White Syndrome and Dilated Cardiomyopathy--A Case Report and Literature Review Based on Emergency Viewpoints=擴大性心肌症和沃爾夫-巴金森-懷特症候群病人接受Verapamil後導致心臟猝死症--一病例報告暨文獻回顧基於急診觀點 |
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作 者 | 張銘遠; 林廷燦; 郭必芳; | 書刊名 | Acta Cardiologica Sinica |
卷 期 | 14:3 民87.07-09 |
頁 次 | 頁154-159 |
分類號 | 415.3165 |
關鍵詞 | 心臟猝死症; 沃爾夫-巴金森-懷特症候群; 附加傳導徑路; 心房顫動; 擴大性心肌症; Sudden cardiac death; Wolff-Parkinson-White syndrome; Accessory pathway; Atrial fibrillation; Dilated cardiomyopathy; |
語 文 | 英文(English) |
中文摘要 | 背景:心臟猝死可能是沃爾夫-巴金森-懷特症候群的最初表現。其機轉是因附加傳導徑路之前向反拗期短而使高心室速率之心房顫動惡化成心室顫動。沃爾夫-巴金森-懷特症候群病人很少發生在年輕人,據我們所知,還沒有關於擴大性心肌症和沃爾夫-巴金森-懷特症候群呈現到院死亡的報告。 方法與結果:在此我們描述一名36歲沃爾夫—巴金森—懷特症候群和擴大性心肌症的男性,因接受Verapamil後,心室速率憎加,轉送至我們急診處時已呈現到院死亡。其心律顯示心室顫動,經立即成功的去震顫心臟電擊,病人恢復了知覺,同時其心律也變成心室早發興奮之心房顫動。隨後經Procainamide處理後,變成心室早發興奮之穩定竇性心率。隔天,病人接受緊急電燒術,成功的切除右後側附加傳導徑路。兩個月後,電氣生理研究(EPS)顯示電燒術成功且無法誘發上心室性頻脈。 結論:基於我們的觀察,具有沃爾夫—巴金森—懷特症候群的病人如發生心房顫動的同時,施予Verapamil會使心室加速而導致心室顫動。因為有此致命的不良反應,所以Verapamil不應用於擴大性心肌症和沃爾夫—巴金森—懷特症候群。 |
英文摘要 | Background. Sudden cardiac death can be the first manifestation of Wolff-Parkinson-White (WPW) syndrome. The underlying mechanism may be atrial fibrillation with a very rapid ventricular rate deteriorating into ventricular fibrillation (VF) because of a short anterograde refractory period of the accessory atrioventricular pathway (AP). VF is a rare but lethal complication in patients with WPW syndrome. Dilated cardiomyopathy (DCM) is an unusual manifestation in young populations. Based on our knowledge, there has been no previous report concerning WPW with DCM presenting death on arrival. Methods and Results. Herein we described a 36-year-old man with WPW syndrome and DCM. He was transferred to our emergency department (ED) due to increased ventricular rate after the intravenous administration of verapamil. On arriving at the hospital, he presented DOA with rhythm strip showing VF. He was promptly and successfully defibrillated and regained consciousness. Cardiac rhythm changed to atrial fibrillation with ventricular preexcitation. After stabilization with the intravenous administration of procainamide, atrial fibrillation converted back to normal sinus rhythm with preexcitation. The following day, the patient underwent urgent radio-frequency ablation (RFA) and the right posterior AP was successfully abolished. Two months later, electrophysiological study (EPS) showed no recurrence of AP conduction and supra-ventricular tachycardia. Conclusions. Based on our observation, the ventricular rate during atrial fibrillation in patients with WPW syndrome may be accelerated in response to verapamil, and VF could occur. Because of this potentially fatal adverse response, verapamil should not be used in patients with Wolff-Parkinson-White syndrome and dilated cardiomyopathy. |
本系統中英文摘要資訊取自各篇刊載內容。