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題 名 | Successful Removal of a Hemangioblastoma from the Medulla Oblongata: Case Report=延腦內血管母細胞瘤之成功摘除:病例報告 |
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作 者 | 盧康; 李道真; 陳維仁; 呂鎮中; | 書刊名 | 長庚醫學 |
卷 期 | 21:4 1998.12[民87.12] |
頁 次 | 頁503-508 |
分類號 | 415.938 |
關鍵詞 | 血管母細胞瘤; 延腦; 顯微手術; Hemangioblastoma; Medulla oblongata; Microsurgical excision; |
語 文 | 英文(English) |
中文摘要 | 血管母細胞瘤可見於von Hippel-Lindau症候群之病人或者單獨發生。此類腫瘤較 常以小腦內囊腫來表現,位於延腦內之血管母細胞瘤則相當罕見,文獻上僅有少數這類腫瘤 被成功摘除之病例報告。本文所報告之病例為一33歲女性,其臨床表現主要為後腦頭痛,步 態穩不及肢體感覺異常。在詳細之放射學檢查之後接受了成功之腫瘤摘除手術,症狀在術後 兩週內消失。血管母細胞瘤由於含有非常豐富之血管,增加了手術之困難度。而位於延腦之 事實也提高了手術之危險性。成功之手術摘除有賴於術前詳細之放射學檢查,包括核磁共振 與血管攝影;及細緻之顯微手術技巧。本文並強調在手術中控制供應腫瘤血液之血管的重要 性。 |
英文摘要 | Hemangioblastomas are histologically benign tumors that occur exclusively within neuraxis, most commonly in the posterior fossa. They are typically cystic tumors located in the cerebellum. Excision of the vascular mural nodules leads to cure. Brain stem lesions are rarely reported. Surgical extirpation of a solid brain stem hemangioblastoma is relatively risky and requires precise microsurgical techniques. We present a woman with a hemangioblastoma embedded in the medulla oblongata. This 33-year-old woman presented with occipital headaches and sensory ataxia. Complete and detailed preoperative imaging studies were followed by successful microsurgical excision of the lesion. The patient recovered completely within 2 weeks after the operation except for mild paresthesia of the legs. Preoperative magnetic resonance imaging and cerebral angiography provided important information regarding the nature, location, and blood suppy of this lesion, which facilitated its total removal. The importance of intraoperative identification and control of the feeding artery of the tumor is emphasized. |
本系統中英文摘要資訊取自各篇刊載內容。