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題 名 | Kikuchi Disease in Systemic Lupus Erythematosus: Clinical Features and Literature Review=Kikuchi氏症與全身性紅班狼瘡: 臨床表徵及文獻回顧 |
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作 者 | 陳怡行; 藍忠亮; | 書刊名 | 微免與感染雜誌 |
卷 期 | 31:3 1998.09[民87.09] |
頁 次 | 頁187-192 |
分類號 | 415.695 |
關鍵詞 | Kikuchi氏症; 全身性紅班狼瘡; Systemic lupus erythematosus; SLE; Kikuchi disease; Histiocytic necrotizing lymphadenitis; Lymphadenopathy; |
語 文 | 英文(English) |
中文摘要 | Kikuchi氏症是一種罕見但良性的淋巴腺炎,好發於年輕女性。本症通常以疼痛或 非痛性頸部淋巴節腫大伴隨發燒為主要之臨床表現。Kikuchi 氏症的病因目前仍未明,且文 獻上僅十七例合併紅斑性狼瘡之報告。 本文報告四例 Kikuchi 氏症合併紅斑性狼瘡之病例 ,為臺灣地區首篇探討 Kikuchi 氏症與紅斑性狼瘡之報告。 四名病患均為女性病人,平均 年齡為 30 歲,平均罹患紅斑性狼瘡之病齡為四年。 一名患者之可粹取核抗原( ENA )為 ribosomal-P 抗體,一名患者為 RNP 抗體,其他兩名之 ENA 為陰性反應。四名患者皆不具 有 SSA 及 SSB 抗體。 其中三名病患( 75 %)發生 Kikuchi 氏症時,伴隨有紅斑性狼瘡 疾病復發的現象。 另一名病患在 Kikuchi 氏症發病時,同時也被診斷出合併有紅斑性狼瘡 。由文獻之報告及我們之經驗,Kikuchi 氏症常在紅斑性狼瘡活動性復發時發生,甚至可為 紅斑性狼瘡之初發症狀。 若同時發生,則可能不是獨立之兩種疾病,而是 Kikuchi 氏症可 能為紅斑性狼瘡的一項臨床表徵。 |
英文摘要 | Kikuchi disease (histiocytic necrotizing lymphadenitis) is a rare, benign entity which predominantly affects young women. The disease usually presents with painful or painless enlarged cervical lymph nodes accompanied with fever. The cause of the disease is uncertain and only 17 cases in the literature have been reported in the past to be associated with systemic lupus erythematosus (SLE). We report four cases of SLE with Kikuchi disease in Taiwan. This is the first report regarding Kikuchi disease and SLE in Taiwan. All patients are female. The mean age is 30 (ranging from 21 to 35 years). The mean history of SLE is 4 years (ranging from 10 days to 8 years). Three of our patients (75%) developed Kikuchi disease accompanied with flare-up of lupus activity, and the other one had Kikuchi disease simultaneously with the onset of SLE. One patient had ribosomal-P antibodies, one had ribonuclear protein (RNP) antibodies and none had antibodies to Ro (SSA) or La (SSB). The cause of association of Kikuchi disease with SLE is still unknown. From our cases, the high frequency of flare-up of lupus disease activity accompanied with the onset of Kikuchi disease and the simultaneous occurrence of these two diseases indicate that they are not independent events. We speculate that Kikuchi disease may be one of the manifestation of SLE. |
本系統中英文摘要資訊取自各篇刊載內容。