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題 名 | Clinical Presentation and Radiographic Diagnosis of Non-traumatic Childhood Diaphragmatic Hernia=非外傷性兒童期橫隔膜疝氣的臨床表現及診斷 |
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作 者 | 馬智盈; 王超然; 勞允澤; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 29:5 2004.10[民93.10] |
頁 次 | 頁239-246 |
分類號 | 417.5401 |
關鍵詞 | 兒童; 腸胃道; 橫隔膜疝氣; Children diagnosis; Children gastrointestrial tract; Hernia diaphragmatic; |
語 文 | 英文(English) |
中文摘要 | 自西元一九九三年至二零零二年間,共有九十位病人於本院診斷為橫隔膜疝氣。其中除了二例為外傷性橫隔膜疝氣外,共有十五例(17.0%,15/88)非外傷性橫隔膜疝氣病例(十三例Bochdalek氏疝氣及二例Morgagni氏疝氣),其臨床表徵發生在新生兒時期之外。所有這十五個病例在新生兒時期都沒有臨床症狀。此類兒童期橫隔膜疝氣可以不具症狀,或者表現各種消化道或呼吸道症狀。將近一半的病例(46.7%)於外科手術時發現疝氣囊。此疝氣囊的表現,可能暗示某個比例上的兒童期橫隔膜疝氣,其實是後天性的,而非先天性的。對於此類病例,X光片檢查是最重要的影像工具,但是在某些病例上尚不足以單靠X光片檢查而獲得正確診斷。本研究當中有六例曾接受鋇劑攝影,並以此獲得正確診斷。兒童期橫隔膜疝氣的預後良好,主因於病人大多沒有或只有輕微之肺臟發育不良。然延誤診斷及治療的時機仍可能導致致命的併發症。本文主要討論兒童期橫隔膜疝氣的臨床及影像表現。 |
英文摘要 | Between years 1993 and 2002, a total of 90 patients were diagnosed as diaphragmatic hernia in our hospital. Excluding 2 cases with traumatic diaphragmatic hernia, there were 15 cases (17.0 %, 15/88) with non-traumatic diaphragmatic hernia in childhood (13 Bochdalek hernias and 2 Morgagni hernias) that presented beyond the neonatal period. All of the 15 patients were without major symptoms in the neonatal period. These patients with childhood diaphragmatic hernia might be asymptomatic or present with various gastrointestinal or respiratory symptoms. Nearly half of the patients (46.7%) had hernia sac found at surgery, which might imply a postnatal cause rather than congenital in a substantial proportion of childhood diaphragmatic hernia. Radiography is the most important imaging modality but may not be adequate for accurate diagnosis in some patients. Barium study was performed in 6 patients and always led to accurate diagnosis in our series. The prognosis of childhood diaphragmatic hernia is good since there is little or no pulmonary hypoplasia. However, delayed diagnosis and treatment may result in life-threatening complications. In this article we discuss the clinical and imaging presentation of childhood diaphragmatic hernia. |
本系統中英文摘要資訊取自各篇刊載內容。