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題 名 | 色素失調症--無水疱病灶期之一病例=Incontinentia Pigmenti--A Case Without Bullous Stage |
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作 者 | 施宗賢; 陳佑甫; 洪志明; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 16:2 1998.06[民87.06] |
頁 次 | 頁108-112 |
分類號 | 415.687 |
關鍵詞 | 色素失調症; Incontinentia pigmenti; |
語 文 | 中文(Chinese) |
中文摘要 | 色素失調症(IP)典型的皮膚表現,初期為紅斑水泡的產生,繼之為疣狀的病灶, 最後再出現潑墨般的色素沉著。我們報告一例非典型的例子,一位5歲大的IP女性患者,其 出生後不久身上出現廣泛的潑墨般的色素沉著,之前則未出現任何水泡病灶。這是一種IP的 罕見型態。 |
英文摘要 | The cutaneous lesions of incontinentia pigmenti(IP) evolve classically in stages beginning with erythematovesicles and bullae followed by verrucous lesions, with eventual macular splashed or whorled hyperpigmentation. We report a 5-year-old case presenting widespread pigmented patches without previous erythematovesicular lesions since birth. This is an uncommon form of IP. |
本系統中英文摘要資訊取自各篇刊載內容。