查詢結果分析
相關文獻
- Magnetic Resonance Findings of Central Nervous System Abnormalities in Incontinentia Pigmenti: A Case Report
- 色素失調症--無水疱病灶期之一病例
- 色素失調症--病例報告及文獻回顧
- Incontinentia Pigmentia: Experience of Seventeen Cases
- 色素失調症合併網膜玻璃體病變--壹男性病例報告
- Incontinentia Pigmenti: A Case Report with Dental Manifestations and Orthodontic Treatment
- Marchiafava-Bignami Disease: CT, MRI and [fee6]Tc HMPAO-SPECT Findings
- De Novo Incontinentia Pigmenti in Female Twins
- 色素失調症合併嚴重缺牙兒童之病例報告
- Incontinentia Pigmenti--A Case Report
頁籤選單縮合
題 名 | Magnetic Resonance Findings of Central Nervous System Abnormalities in Incontinentia Pigmenti: A Case Report=色素失調症在腦部磁振造影上的表徵--病例報告 |
---|---|
作 者 | 梁恆; 陳偉斌; 吳汝濱; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 25:1 2000.02[民89.02] |
頁 次 | 頁23-25 |
分類號 | 414.93 |
關鍵詞 | 色素失調症; 大腦磁振造影; Incontinentia pigmenti; Brain MR; |
語 文 | 英文(English) |
中文摘要 | 色素失調症為一罕見之神經與皮膚病變, 其臨床之症狀在出生不久後, 眼睛、牙齒、頭髮缺陷及皮膚黑色素過分沈著同時存在。在報告中超過50%之病患有腦部之異常發育。磁振造影可偵測腦部之異常表徵。 |
英文摘要 | Incontinentia pigmenti, or Bloch-Sulzberger syndrome is a rare neurocutaneous disease. The clinical manifestations begin at or shortly after birth. The central nervous system manifestations include seizures, spastic paralysis, mental retardation, microcephaly and hydrocephalus. The other clinical features include congenital skin lesions, dental and skeletal dysplasia. The occular manifestation of retinal arteriolar occulsion with subsequent retinal hemorrhage and infarction is quite frequent. Magnetic resonance imaging and Magnetic resonance (MR) angiography are valuable in detecting abnormalities of the brain parenchyma and cerebral circulation. More than 50% of the patients have central nervous system (CNS) involvement with MR abnormality. We present the cerebral magnetic resonance imaging (MRI) findings in a female neonate. |
本系統中英文摘要資訊取自各篇刊載內容。